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Debra A. Long Priel
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Journal Articles

A phase 1 clinical trial of long-term, low-dose treatment of WHIM syndrome with the CXCR4 antagonist plerixafor

Clinical Trials & Observations
David H. McDermott, Qian Liu, Daniel Velez, Lizbeeth Lopez, Sandra Anaya-O’Brien, Jean Ulrick, Nana Kwatemaa, Judy Starling, Thomas A. Fleisher, Debra A. Long Priel, Melissa A. Merideth, Robert L. Giuntoli, Moses O. Evbuomwan, Patricia Littel, Martha M. Marquesen, Dianne Hilligoss, Rosamma DeCastro, George J. Grimes, Samuel T. Hwang, Stefania Pittaluga, Katherine R. Calvo, Pamela Stratton, Edward W. Cowen, Douglas B. Kuhns, Harry L. Malech, Philip M. Murphy
Journal: Blood
Blood (2014) 123 (15): 2308–2316.
https://doi.org/10.1182/blood-2013-09-527226
Published: 2014
Includes: Supplemental data
Journal Articles

Loss-of-function of the protein kinase C δ (PKCδ) causes a B-cell lymphoproliferative syndrome in humans

Hye Sun Kuehn, Julie E. Niemela, Andreia Rangel-Santos, Mingchang Zhang, Stefania Pittaluga, Jennifer L. Stoddard, Ashleigh A. Hussey, Moses O. Evbuomwan, Debra A. Long Priel, Douglas B. Kuhns, C. Lucy Park, Thomas A. Fleisher, Gulbu Uzel, João B. Oliveira
Journal: Blood
Blood (2013) 121 (16): 3117–3125.
https://doi.org/10.1182/blood-2012-12-469544
Published: 2013
Includes: Supplemental data
Journal Articles

The CXCR4 antagonist plerixafor corrects panleukopenia in patients with WHIM syndrome

Clinical Trials & Observations
David H. McDermott, Qian Liu, Jean Ulrick, Nana Kwatemaa, Sandra Anaya-O'Brien, Scott R. Penzak, Joao Oliveira Filho, Debra A. Long Priel, Corin Kelly, Mary Garofalo, Patricia Littel, Martha M. Marquesen, Diane Hilligoss, Rosamma DeCastro, Thomas A. Fleisher, Douglas B. Kuhns, Harry L. Malech, Philip M. Murphy
Journal: Blood
Blood (2011) 118 (18): 4957–4962.
https://doi.org/10.1182/blood-2011-07-368084
Published: 2011
Includes: Supplemental data
Journal Articles

Severe congenital neutropenia resulting from G6PC3 deficiency with increased neutrophil CXCR4 expression and myelokathexis

Clinical Trials & Observations
David H. McDermott, Suk See De Ravin, Hyun Sik Jun, Qian Liu, Debra A. Long Priel, Pierre Noel, Clifford M. Takemoto, Teresa Ojode, Scott M. Paul, Kimberly P. Dunsmore, Dianne Hilligoss, Martha Marquesen, Jean Ulrick, Douglas B. Kuhns, Janice Y. Chou, Harry L. Malech, Philip M. Murphy
Journal: Blood
Blood (2010) 116 (15): 2793–2802.
https://doi.org/10.1182/blood-2010-01-265942
Published: 2010
Journal Articles

Retrovirus gene therapy for X-linked chronic granulomatous disease can achieve stable long-term correction of oxidase activity in peripheral blood neutrophils

Elizabeth M. Kang, Uimook Choi, Narda Theobald, Gilda Linton, Debra A. Long Priel, Doug Kuhns, Harry L. Malech
Journal: Blood
Blood (2010) 115 (4): 783–791.
https://doi.org/10.1182/blood-2009-05-222760
Published: 2010
Includes: Supplemental data