Hereditary Benign Erythroreticulosis

In the province of Västerbotten, Northern Sweden, we have observed a blood disease formerly unknown in Europe. It is characterized by:

1. A non-hemolytic normochromic anemia with a low or normal reticulocyte count and without indications of reduced or increased activity of either granulocytopoiesis or thrombocytopoiesis.

2. A characteristic bone marrow picture corresponding to the di Guglielmo disorder.

3. An abnormal hemoglobin.

4. A favorable clinical course, but refractory to therapy.

5. An hereditary component.