Figure 4.
Figure 4. The effect of fresh frozen plasma (FFP) infusions on the platelet count in a patient with severe constitutional deficiency of von Willebrand factor (VWF)-cleaving protease. / This patient had no acute episode of thrombotic thrombocytopenic purpura (TTP) before age 20. The first TTP event was followed by several acute bouts, leading to a diagnosis of chronic relapsing TTP caused by severe VWF-cleaving protease deficiency. After the last relapse at age 36, the patient received 8 months of prophylactic treatment with 2 units of FFP every third week, and subsequently with only 1 unit of FFP every 2 weeks. / Reprinted with permission from Furlan M, Lämmle B. Best Pract Res Clin Haematol. 2001;14:437-454.

The effect of fresh frozen plasma (FFP) infusions on the platelet count in a patient with severe constitutional deficiency of von Willebrand factor (VWF)-cleaving protease.

This patient had no acute episode of thrombotic thrombocytopenic purpura (TTP) before age 20. The first TTP event was followed by several acute bouts, leading to a diagnosis of chronic relapsing TTP caused by severe VWF-cleaving protease deficiency. After the last relapse at age 36, the patient received 8 months of prophylactic treatment with 2 units of FFP every third week, and subsequently with only 1 unit of FFP every 2 weeks.

Reprinted with permission from Furlan M, Lämmle B. Best Pract Res Clin Haematol. 2001;14:437-454.

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