Table 2.

Diagnostic criteria for HLH20 

Diagnostic criteria for HLH20

Supportive evidence is cerebral symptoms with moderate pleocytosis and/or elevated protein, elevated transaminases, bilirubin, and lactate dehydrogenase. sCD indicates soluble interleukin-2 receptor.

*A higher cutoff of 3000 μg/L has been suggested as being more specific.21 

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