The GFTP of the new LAD II patient is nonfunctional. (A) Fibroblasts derived from a healthy control donor and from patient G were stained with AAL. Perinuclear fucoslyation in the Golgi is seen in healthy but not in patient cells. (B) Complementation of LAD II fibroblasts with green fluorescent protein (GFP)–tagged GFTPs of a healthy donor (wild-type), the Turkish LAD II patient, and patient G, respectively. Cells were double-stained with anti-GFP and AAL. One representative experiment of 6 is shown. Bars represent 10 μm.