Features of Budd-Chiari syndrome in PNH. (A) A pie chart illustrates the type of TEs. (B) A cartoon showcases the anatomic site of origin of thromboses. (C) Left panel shows magnetic resonance imaging (MRI) of a 59-year-old man, whereby on the axial postcontrast VIBE (volumetric interpolated breath-hold examination), the hepatic veins are decreased in caliber (thin arrows) and demonstrate peripheral pruning, however there is no residual hepatic venous filling defect to suggest thrombus. The intrahepatic inferior vena cava (IVC; thick arrow) is significantly narrowed without IVC thrombosis. On the right, a Doppler ultrasound image of the IVC of an 89-year-old male shows the hypoechoic and nonocclusive thrombus in the lumen (arrow). (D) A swimmer plot illustrates the longitudinal follow-up, and anticomplement and anticoagulation strategies in patients experiencing TEs in our cohort. ∗Patients for whom precise dates on subsequent thrombotic events (5 episodes for UPN 9 and 3 episodes for UPN 13) are lacking.