Etoposide/dexamethasone therapy for HLH (based on HLH94): initial therapy (weeks 1-8) for patients with familial/ idiopathic HLH. CBC, complete blood count; CNS, central nervous system; HC, hydrocortisone; IgG, immunoglobulin G; IT, intrathecal therapy; IVIG, intravenous immunoglobulin; MTX, methotrexate; PJP, pneumocystis jirovecii pneumoni; PPI, proton pump inhibitors; PT, prothrombin time; PTT, partial thromboplastin time.