Table 1

Baseline clinical and laboratory variables in 1193 SCD patients

VariableValue
Age at first encounter, median (IQR), y 24 (17-35) 
Sex, male/female, n (%) 515 (43.2)/678 (56.8) 
Race, African American, n (%) 1123 (94.1) 
Sickle cell genotype, n (%)  
 HbSS/SB0-thalassemia 831 (69.7) 
 HbSC 290 (24.3) 
 HbSB+-thalassemia 69 (5.8) 
 Other 3 (0.3) 
Hydroxyurea by sickle cell genotype, n/N (%)  
 Total 659/1193 (55.2) 
 HbSS/SB0- thalassemia 560/831 (67.4) 
 HbSC 77/290 (26.6) 
 HbSB+-thalassemia 22/69 (31.9) 
 Other 0/3 (0) 
VariableValue
Age at first encounter, median (IQR), y 24 (17-35) 
Sex, male/female, n (%) 515 (43.2)/678 (56.8) 
Race, African American, n (%) 1123 (94.1) 
Sickle cell genotype, n (%)  
 HbSS/SB0-thalassemia 831 (69.7) 
 HbSC 290 (24.3) 
 HbSB+-thalassemia 69 (5.8) 
 Other 3 (0.3) 
Hydroxyurea by sickle cell genotype, n/N (%)  
 Total 659/1193 (55.2) 
 HbSS/SB0- thalassemia 560/831 (67.4) 
 HbSC 77/290 (26.6) 
 HbSB+-thalassemia 22/69 (31.9) 
 Other 0/3 (0) 

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