Table 1.

CVID subjects sequenced in 3 cohorts

ParametersUSSwedenIran
235 128 208 
Males, n 101 63 113 
Females, n 134 65 95 
Median age (range), y 44 (5-85) 49.5 (4-90) 9 (1-65) 
Known consanguineous, n (%) 129 (63) 
Relatives with immune defects, n 14 23 
Gene candidates identified, n (%) 74 (31) 46 (36) 112 (54) 
ParametersUSSwedenIran
235 128 208 
Males, n 101 63 113 
Females, n 134 65 95 
Median age (range), y 44 (5-85) 49.5 (4-90) 9 (1-65) 
Known consanguineous, n (%) 129 (63) 
Relatives with immune defects, n 14 23 
Gene candidates identified, n (%) 74 (31) 46 (36) 112 (54) 
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