Molecular, phenotypic, and clinical characteristics of the Ig V gene-defined B-cell chronic lymphocytic leukemia (B-CLL) subgroups.*
. | Subgroup I . | Subgroup II . |
---|---|---|
* Subgroup I is defined by the expression of unmutated (< 2% difference from germline counterpart) BCRs, and Subgroup II by the expression of mutated (≥ 2% difference from germ line) BCRs. Patients in Subgroup I experience a much more aggressive clinical course. | ||
Abbreviations: Ig, immunoglobulin; BCR, B-cell receptor. | ||
Stage at presentation | Often Rai intermediate/high risk | Often Rai low risk |
Age at presentation | No difference | No difference |
Gender | More males | M = F |
Lymphocyte doubling time | Frequently < 12 months | Frequently > 12 months |
V gene mutations | Few or none | Significant numbers |
Antigen selection | Yes | Yes |
ZAP70 expression | High | Low |
CD38 expression | High | Low |
Activation markers | 38+/69+ | 71+/62L+ |
Telomere length | Uniformly short | Diverse lengths |
Telomerase activity | High | Low |
Retention of BCR signaling | Yes | No |
Ongoing Ig V gene mutations | Yes | Yes |
Intermittent expression of AID | Yes | Yes |
Chromosomal abnormalities | Poor prognosis | Better prognosis |
Treatment requirement | Usual | Unusual |
. | Subgroup I . | Subgroup II . |
---|---|---|
* Subgroup I is defined by the expression of unmutated (< 2% difference from germline counterpart) BCRs, and Subgroup II by the expression of mutated (≥ 2% difference from germ line) BCRs. Patients in Subgroup I experience a much more aggressive clinical course. | ||
Abbreviations: Ig, immunoglobulin; BCR, B-cell receptor. | ||
Stage at presentation | Often Rai intermediate/high risk | Often Rai low risk |
Age at presentation | No difference | No difference |
Gender | More males | M = F |
Lymphocyte doubling time | Frequently < 12 months | Frequently > 12 months |
V gene mutations | Few or none | Significant numbers |
Antigen selection | Yes | Yes |
ZAP70 expression | High | Low |
CD38 expression | High | Low |
Activation markers | 38+/69+ | 71+/62L+ |
Telomere length | Uniformly short | Diverse lengths |
Telomerase activity | High | Low |
Retention of BCR signaling | Yes | No |
Ongoing Ig V gene mutations | Yes | Yes |
Intermittent expression of AID | Yes | Yes |
Chromosomal abnormalities | Poor prognosis | Better prognosis |
Treatment requirement | Usual | Unusual |