Patient characteristics
Patient . | Age at diagnosis, y . | Diagnosis . | Sex . | Evidence of hemophagocytosis . | Liver disease . | Biallelic perforin mutations . | Monoallelic perforin mutations . |
---|---|---|---|---|---|---|---|
1 | 21 | NHL | M | Yes | No | Yes | No |
2 | 7 | HD/B-NHL | M | Yes | Yes | Yes | No |
3 | 7 | T-NHL | F | Yes | Yes | Yes | No |
4 | 18 | T-NHL | F | Yes | No | Yes | No |
5 | 6 | HD/B-NHL | F | No | No | No | No |
6 | 10 | B-NHL | F | No | Yes | No | Yes |
7 | 3 | B-NHL | M | Yes | Yes | No | No |
8 | 17 | T-NHL | F | Yes | No | No | No |
9 | 10 | T-NHL | M | No | No | No | Yes |
10 | 7 | T-NHL | M | No | No | No | No |
11 | 27 | B-NHL | M | No | Yes | No | Yes |
12 | 22 | T-NHL | M | No | Yes | No | No |
13 | 5 | T-NHL | F | No | Yes | No | No |
14 | 19 | HD | M | No | No | No | Yes |
15 | 17 | T-NHL | F | No | No | No | No |
16 | 58 | T-NHL | M | No | No | No | No |
17 | 6 | B-NHL | F | No | No | No | No |
18 | 7 | T-NHL | M | No | No | No | No |
19 | 10 | B-NHL | F | No | Yes | No | No |
20 | 8 | B-NHL/HD | M | No | No | No | No |
21 | 30 | T-NHL | M | No | No | No | No |
22 | 40 | HD | M | No | No | No | No |
23 | 38 | T-NHL | M | Yes | No | No | No |
24 | 51 | B-NHL | F | No | No | No | No |
25 | 10 | B-NHL | F | No | No | No | No |
26 | 40 | NHL | F | No | Yes | No | No |
27 | 15 | B-NHL | M | No | No | No | No |
28 | 6 | B-NHL | M | No | Yes | No | No |
29 | 50 | NHL | F | No | No | No | No |
Patient . | Age at diagnosis, y . | Diagnosis . | Sex . | Evidence of hemophagocytosis . | Liver disease . | Biallelic perforin mutations . | Monoallelic perforin mutations . |
---|---|---|---|---|---|---|---|
1 | 21 | NHL | M | Yes | No | Yes | No |
2 | 7 | HD/B-NHL | M | Yes | Yes | Yes | No |
3 | 7 | T-NHL | F | Yes | Yes | Yes | No |
4 | 18 | T-NHL | F | Yes | No | Yes | No |
5 | 6 | HD/B-NHL | F | No | No | No | No |
6 | 10 | B-NHL | F | No | Yes | No | Yes |
7 | 3 | B-NHL | M | Yes | Yes | No | No |
8 | 17 | T-NHL | F | Yes | No | No | No |
9 | 10 | T-NHL | M | No | No | No | Yes |
10 | 7 | T-NHL | M | No | No | No | No |
11 | 27 | B-NHL | M | No | Yes | No | Yes |
12 | 22 | T-NHL | M | No | Yes | No | No |
13 | 5 | T-NHL | F | No | Yes | No | No |
14 | 19 | HD | M | No | No | No | Yes |
15 | 17 | T-NHL | F | No | No | No | No |
16 | 58 | T-NHL | M | No | No | No | No |
17 | 6 | B-NHL | F | No | No | No | No |
18 | 7 | T-NHL | M | No | No | No | No |
19 | 10 | B-NHL | F | No | Yes | No | No |
20 | 8 | B-NHL/HD | M | No | No | No | No |
21 | 30 | T-NHL | M | No | No | No | No |
22 | 40 | HD | M | No | No | No | No |
23 | 38 | T-NHL | M | Yes | No | No | No |
24 | 51 | B-NHL | F | No | No | No | No |
25 | 10 | B-NHL | F | No | No | No | No |
26 | 40 | NHL | F | No | Yes | No | No |
27 | 15 | B-NHL | M | No | No | No | No |
28 | 6 | B-NHL | M | No | Yes | No | No |
29 | 50 | NHL | F | No | No | No | No |
NHL indicates non-Hodgkin lymphoma; M, male; HD, Hodgkin disease; B-NHL, B-cell non-Hodgkin lymphoma; T-NHL, T-cell non-Hodgkin lymphoma; and F, female.