Patient characteristics at transplantation for 33 patients younger than 17 years
UPN . | Sex . | Country . | Age, y . | No. of Tx . | CI . | Ferritin, ng/mL . | GOT, U/L . | GPT, U/L . | LIC, mg/g dry weight . | FS . | CAH . |
---|---|---|---|---|---|---|---|---|---|---|---|
1211 | F | Albania | 16 | 230 | 100 | 2591 | 49 | 60 | 30.9 | Mo | No |
1230 | F | Italy | 16 | 290 | 100 | 3221 | 42 | 60 | 13.6 | Se | Yes |
1231 | F | Kuwait | 11 | 75 | 100 | 1900 | 16 | 32 | 8.2 | Mi | No |
1236 | M | Saudi Arabia | 16 | 200 | 100 | 2557 | 31 | 29 | 28.3 | Ci | Yes |
1262 | F | Albania | 12 | 200 | 100 | 4533 | 77 | 55 | 30.1 | Se | No |
1288 | M | Saudi Arabia | 12 | 150 | 37 | 968 | 41 | 43 | 15.8 | Mi | No |
1292 | M | Kuwait | 9 | 80 | 100 | 1624 | 34 | 31 | 24.5 | Mo | Yes |
1319 | M | Syria | 16 | 200 | 100 | 1087 | 27 | 20 | 7.8 | Ci | No |
1324 | F | Pakistan | 10 | 125 | 13 | 1391 | 35 | 24 | 20.5 | Mo | Yes |
1331 | F | Kuwait | 12 | 118 | 100 | 3558 | 47 | 72 | 38.1 | Ci | Yes |
1339 | F | Lebanon | 12 | 100 | 100 | 3158 | 34 | 45 | 26.4 | Mo | Yes |
1342 | F | Palestine | 6 | 90 | 54 | 1967 | 37 | 57 | 28.7 | Mo | No |
1347 | F | Kuwait | 4 | 18 | 100 | 4016 | 220 | 260 | 15.5 | Se | No |
1357 | F | Saudi Arabia | 9 | 80 | 10 | 1140 | 31 | 28 | 7.5 | Mi | No |
1362 | M | Libya | 9 | 18 | 100 | 1226 | 30 | 51 | 0.9 | Mo | No |
1363 | M | Nepal | 4 | 6 | 100 | 1925 | 67 | 65 | 15.7 | Mi | No |
1371 | F | Albania | 14 | 130 | 100 | 2067 | 48 | 69 | 30.5 | Se | No |
1372 | F | Kuwait | 15 | 200 | 100 | 6300 | 13 | 13 | 30.2 | Mo | No |
1374 | M | Jordan | 7 | 30 | 100 | 4463 | 66 | 88 | 40.1 | Se | No |
1375 | M | Italy | 10 | 130 | 5 | 2721 | 27 | 52 | 14.4 | Se | No |
1389 | F | Iran | 14 | 150 | 49 | 2835 | 29 | 16 | 19 | Mi | No |
1409 | M | Iraq | 5 | 70 | 100 | 2338 | 55 | 93 | 20.3 | Se | No |
1413 | F | Kuwait | 9 | 106 | 100 | 2449 | 32 | 27 | 9.3 | Mo | Yes |
1414 | F | Saudi Arabia | 15 | 120 | 100 | 5306 | 12 | 18 | 14.4 | Mo | Yes |
1427 | F | Italy | 14 | 280 | 100 | 3386 | 32 | 30 | 17.4 | Mo | No |
1429 | M | Romania | 11 | 10 | 100 | 1000 | 39 | 37 | 4.9 | Mo | Yes |
1435 | M | Pakistan | 10 | 60 | 100 | 3492 | 16 | 23 | 15.8 | Mo | Yes |
1444 | M | Palestine | 8 | 90 | 100 | 3231 | 51 | 48 | 20.1 | Se | Yes |
1445 | F | Palestine | 11 | 120 | 100 | 953 | 38 | 26 | 2.7 | Mo | Yes |
1448 | M | Palestine | 16 | 130 | 100 | 4578 | 47 | 38 | 38.1 | Ci | Yes |
1449 | M | Palestine | 15 | 80 | 100 | 2120 | 31 | 43 | 4.2 | Mi | No |
1454 | M | Palestine | 5 | 60 | 100 | 1619 | 31 | 42 | 18.8 | Mo | Yes |
1457 | M | Albania | 12 | 140 | 100 | 1257 | 79 | 45 | 14.1 | Mo | Yes |
UPN . | Sex . | Country . | Age, y . | No. of Tx . | CI . | Ferritin, ng/mL . | GOT, U/L . | GPT, U/L . | LIC, mg/g dry weight . | FS . | CAH . |
---|---|---|---|---|---|---|---|---|---|---|---|
1211 | F | Albania | 16 | 230 | 100 | 2591 | 49 | 60 | 30.9 | Mo | No |
1230 | F | Italy | 16 | 290 | 100 | 3221 | 42 | 60 | 13.6 | Se | Yes |
1231 | F | Kuwait | 11 | 75 | 100 | 1900 | 16 | 32 | 8.2 | Mi | No |
1236 | M | Saudi Arabia | 16 | 200 | 100 | 2557 | 31 | 29 | 28.3 | Ci | Yes |
1262 | F | Albania | 12 | 200 | 100 | 4533 | 77 | 55 | 30.1 | Se | No |
1288 | M | Saudi Arabia | 12 | 150 | 37 | 968 | 41 | 43 | 15.8 | Mi | No |
1292 | M | Kuwait | 9 | 80 | 100 | 1624 | 34 | 31 | 24.5 | Mo | Yes |
1319 | M | Syria | 16 | 200 | 100 | 1087 | 27 | 20 | 7.8 | Ci | No |
1324 | F | Pakistan | 10 | 125 | 13 | 1391 | 35 | 24 | 20.5 | Mo | Yes |
1331 | F | Kuwait | 12 | 118 | 100 | 3558 | 47 | 72 | 38.1 | Ci | Yes |
1339 | F | Lebanon | 12 | 100 | 100 | 3158 | 34 | 45 | 26.4 | Mo | Yes |
1342 | F | Palestine | 6 | 90 | 54 | 1967 | 37 | 57 | 28.7 | Mo | No |
1347 | F | Kuwait | 4 | 18 | 100 | 4016 | 220 | 260 | 15.5 | Se | No |
1357 | F | Saudi Arabia | 9 | 80 | 10 | 1140 | 31 | 28 | 7.5 | Mi | No |
1362 | M | Libya | 9 | 18 | 100 | 1226 | 30 | 51 | 0.9 | Mo | No |
1363 | M | Nepal | 4 | 6 | 100 | 1925 | 67 | 65 | 15.7 | Mi | No |
1371 | F | Albania | 14 | 130 | 100 | 2067 | 48 | 69 | 30.5 | Se | No |
1372 | F | Kuwait | 15 | 200 | 100 | 6300 | 13 | 13 | 30.2 | Mo | No |
1374 | M | Jordan | 7 | 30 | 100 | 4463 | 66 | 88 | 40.1 | Se | No |
1375 | M | Italy | 10 | 130 | 5 | 2721 | 27 | 52 | 14.4 | Se | No |
1389 | F | Iran | 14 | 150 | 49 | 2835 | 29 | 16 | 19 | Mi | No |
1409 | M | Iraq | 5 | 70 | 100 | 2338 | 55 | 93 | 20.3 | Se | No |
1413 | F | Kuwait | 9 | 106 | 100 | 2449 | 32 | 27 | 9.3 | Mo | Yes |
1414 | F | Saudi Arabia | 15 | 120 | 100 | 5306 | 12 | 18 | 14.4 | Mo | Yes |
1427 | F | Italy | 14 | 280 | 100 | 3386 | 32 | 30 | 17.4 | Mo | No |
1429 | M | Romania | 11 | 10 | 100 | 1000 | 39 | 37 | 4.9 | Mo | Yes |
1435 | M | Pakistan | 10 | 60 | 100 | 3492 | 16 | 23 | 15.8 | Mo | Yes |
1444 | M | Palestine | 8 | 90 | 100 | 3231 | 51 | 48 | 20.1 | Se | Yes |
1445 | F | Palestine | 11 | 120 | 100 | 953 | 38 | 26 | 2.7 | Mo | Yes |
1448 | M | Palestine | 16 | 130 | 100 | 4578 | 47 | 38 | 38.1 | Ci | Yes |
1449 | M | Palestine | 15 | 80 | 100 | 2120 | 31 | 43 | 4.2 | Mi | No |
1454 | M | Palestine | 5 | 60 | 100 | 1619 | 31 | 42 | 18.8 | Mo | Yes |
1457 | M | Albania | 12 | 140 | 100 | 1257 | 79 | 45 | 14.1 | Mo | Yes |
UPN indicates unique patient number; No. of Tx, number of red cell transfusions before transplantation; CI, chelation index; GOT, glutamic-oxaloacetic transaminase; GPT, glutamic-pyruvic transaminase; LIC, liver iron concentration; FS, portal fibrosis (Mi, mild; Mo, moderate; Se, severe; Ci, cirrhotic); CAH, chronic active hepatitis (yes, present; no, absent)