Diagnostic criteria for HLH
Type of diagnosis . | Criteria . |
---|---|
Clinical | Fever and splenomegaly |
Laboratory | Cytopenias in at least 2 cell lineages and hypertryglyceridemia or hypofibrinogenemia |
Histologic | Hemophagocytosis in bone marrow or spleen or lymph node |
Type of diagnosis . | Criteria . |
---|---|
Clinical | Fever and splenomegaly |
Laboratory | Cytopenias in at least 2 cell lineages and hypertryglyceridemia or hypofibrinogenemia |
Histologic | Hemophagocytosis in bone marrow or spleen or lymph node |
Adapted from Hentler et al.4