Table 1.

Diagnostic criteria for HLH


Type of diagnosis

Criteria
Clinical   Fever and splenomegaly  
Laboratory   Cytopenias in at least 2 cell lineages and hypertryglyceridemia or hypofibrinogenemia  
Histologic
 
Hemophagocytosis in bone marrow or spleen or lymph node
 

Type of diagnosis

Criteria
Clinical   Fever and splenomegaly  
Laboratory   Cytopenias in at least 2 cell lineages and hypertryglyceridemia or hypofibrinogenemia  
Histologic
 
Hemophagocytosis in bone marrow or spleen or lymph node
 

Adapted from Hentler et al.