Table 1.

Surface marker analysis of the XL-EDA-ID patient's PBMCs




%

Healthy control, %
CD3   41.2   66.1 ± 5.9  
CD4   8.0   37.7 ± 9.6  
CD8   31.8   23.7 ± 4.2  
TCRαβ   38.0   56.5 ± 10.5  
TCRγδ   3.0   9.5 ± 5.5  
CD4+CD45RA   1.6   32.5 ± 10.8  
CD4+CD45RO   7.2   10.2 ± 3.5  
CD8+CD45RA   32.3   20.7 ± 5.1  
CD8+CD45RO   9.9   7.6 ± 3.6  
CD4+CD25+  2.2   5.5 ± 1.2  
CD19   32.9   23.1 ± 4.1  
CD20   32.6   23.3 ± 4.0  
CD19/Sm-IgG   0.2   1.2 ± 1.0  
CD19/Sm-IgA   0.4   0.6 ± 0.5  
CD19/Sm-IgM   32.1   21.0 ± 3.8  
CD19/Sm-IgD   32.1   20.8 ± 3.7  
CD16   25.0   10.5 ± 5.2  
CD56
 
24.9
 
9.2 ± 4.8
 



%

Healthy control, %
CD3   41.2   66.1 ± 5.9  
CD4   8.0   37.7 ± 9.6  
CD8   31.8   23.7 ± 4.2  
TCRαβ   38.0   56.5 ± 10.5  
TCRγδ   3.0   9.5 ± 5.5  
CD4+CD45RA   1.6   32.5 ± 10.8  
CD4+CD45RO   7.2   10.2 ± 3.5  
CD8+CD45RA   32.3   20.7 ± 5.1  
CD8+CD45RO   9.9   7.6 ± 3.6  
CD4+CD25+  2.2   5.5 ± 1.2  
CD19   32.9   23.1 ± 4.1  
CD20   32.6   23.3 ± 4.0  
CD19/Sm-IgG   0.2   1.2 ± 1.0  
CD19/Sm-IgA   0.4   0.6 ± 0.5  
CD19/Sm-IgM   32.1   21.0 ± 3.8  
CD19/Sm-IgD   32.1   20.8 ± 3.7  
CD16   25.0   10.5 ± 5.2  
CD56
 
24.9
 
9.2 ± 4.8
 

Surface markers of the XL-EDA-ID patient PBMCs are shown as a percentage of gated mononuclear cells. Health control values are based on 1- to 6-year-old children for whom informed consent was obtained. Health control values are shown as mean ± SD. Sm indicates surface membrane.

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