Table 4.

Tabular summary of survival data for subjects with SS and Sβ°



Overall survival

SCD-related survival

Stroke-free survival
Age
% survival
95% CI
% survival
95% CI
% survival
95% CI
6 mo   100   —   100   —   100   —  
1 y   99.5   98.8-100   99.8   99.3-100   99.8   99.3-100  
2 y   98.5   97.3-99.7   99.5   98.8-100   99.5   98.8-100  
4 y   97.7   96.2-99.2   98.6   97.5-99.9   96.3   94.3-98.3  
6 y   95   92.7-97.3   96.3   94.2-98.4   94.3   91.8-96.8  
8 y   94.6   92.1-97.1   95.9   93.7-98.1   91.3   88.0-94.6  
10 y   94.6   92.1-97.1   95.9   93.7-98.1   91.6   88.4-94.5  
12 y   94.6   92.1-97.1   95.9   93.7-98.1   90.1   86.5-93.7  
14 y   93   89.7-96.3   94.9   92.0-97.8   88.5   84.3-92.7  
16 y   91.7   87.6-95.8   93.6   89.8-97.4   88.5   84.3-92.7  
18 y
 
85.6
 
73.4-97.8
 
93.6
 
89.8-97.4
 
88.5
 
84.3-92.7
 


Overall survival

SCD-related survival

Stroke-free survival
Age
% survival
95% CI
% survival
95% CI
% survival
95% CI
6 mo   100   —   100   —   100   —  
1 y   99.5   98.8-100   99.8   99.3-100   99.8   99.3-100  
2 y   98.5   97.3-99.7   99.5   98.8-100   99.5   98.8-100  
4 y   97.7   96.2-99.2   98.6   97.5-99.9   96.3   94.3-98.3  
6 y   95   92.7-97.3   96.3   94.2-98.4   94.3   91.8-96.8  
8 y   94.6   92.1-97.1   95.9   93.7-98.1   91.3   88.0-94.6  
10 y   94.6   92.1-97.1   95.9   93.7-98.1   91.6   88.4-94.5  
12 y   94.6   92.1-97.1   95.9   93.7-98.1   90.1   86.5-93.7  
14 y   93   89.7-96.3   94.9   92.0-97.8   88.5   84.3-92.7  
16 y   91.7   87.6-95.8   93.6   89.8-97.4   88.5   84.3-92.7  
18 y
 
85.6
 
73.4-97.8
 
93.6
 
89.8-97.4
 
88.5
 
84.3-92.7
 

-indicates not applicable.

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