Table 1.

Expression of CD117, tryptase, and SERPINB6 in relation to subtype of mastocytosis



Patient characteristics

Positive tumor cells, %
Diagnosis
Site of biopsy
Sex
Age
CD117
Tryptase
SERPINB6
Cutaneous mastocytosis, n = 13       
Urticaria pigmentosa   Trunk   M   21 y   75-100   75-100   75-100  
Urticaria pigmentosa   Leg   F   30 y   75-100   75-100   50-75  
Urticaria pigmentosa   Arm   F   26 y   75-100   75-100   75-100  
Urticaria pigmentosa   Trunk   M   45 y   75-100   75-100   25-50  
Urticaria pigmentosa   Leg   F   27 y   75-100   75-100   5-25  
Diffuse cutaneous mastocytosis   Trunk   F   9 mo   75-100   75-100   75-100  
Diffuse cutaneous mastocytosis   Buttock   M   7 mo   75-100   50-75   75-100  
Diffuse cutaneous mastocytosis   Trunk   F   9 mo   75-100   25-50   50-75  
Diffuse cutaneous mastocytosis   Trunk   F   6 mo   75-100   25-50   75-100  
Mastocytoma   Foot   M   11 mo   75-100   75-100   75-100  
Mastocytoma   Leg   M   6 mo   75-100   5-25   75-100  
Mastocytoma   Trunk   M   9 mo   75-100   25-50   75-100  
Mastocytoma   Trunk   F   6 mo   75-100   50-75   75-100  
Systemic mastocytosis, n = 2       
Systemic mastocytosis   Colon   M   40 y   75-100   50-75   50-75  
Systemic mastocytosis
 
Bone marrow
 
F
 
53 y
 
75-100
 
50-75
 
50-75
 


Patient characteristics

Positive tumor cells, %
Diagnosis
Site of biopsy
Sex
Age
CD117
Tryptase
SERPINB6
Cutaneous mastocytosis, n = 13       
Urticaria pigmentosa   Trunk   M   21 y   75-100   75-100   75-100  
Urticaria pigmentosa   Leg   F   30 y   75-100   75-100   50-75  
Urticaria pigmentosa   Arm   F   26 y   75-100   75-100   75-100  
Urticaria pigmentosa   Trunk   M   45 y   75-100   75-100   25-50  
Urticaria pigmentosa   Leg   F   27 y   75-100   75-100   5-25  
Diffuse cutaneous mastocytosis   Trunk   F   9 mo   75-100   75-100   75-100  
Diffuse cutaneous mastocytosis   Buttock   M   7 mo   75-100   50-75   75-100  
Diffuse cutaneous mastocytosis   Trunk   F   9 mo   75-100   25-50   50-75  
Diffuse cutaneous mastocytosis   Trunk   F   6 mo   75-100   25-50   75-100  
Mastocytoma   Foot   M   11 mo   75-100   75-100   75-100  
Mastocytoma   Leg   M   6 mo   75-100   5-25   75-100  
Mastocytoma   Trunk   M   9 mo   75-100   25-50   75-100  
Mastocytoma   Trunk   F   6 mo   75-100   50-75   75-100  
Systemic mastocytosis, n = 2       
Systemic mastocytosis   Colon   M   40 y   75-100   50-75   50-75  
Systemic mastocytosis
 
Bone marrow
 
F
 
53 y
 
75-100
 
50-75
 
50-75
 

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