Table 1.

Clinical characterization of patients



Age, y/sex


Duration, y

Before IVIG, muscle involvement

Before IVIG, skin involvement

IVIG cycles

Final outcome, muscle involvement

Final outcome, skin involvement
Patient
Diagnosis
Score*
CK level
Extent
Pruritus
Score*
CK level
Extent
Pruritus
A   34/F   ADM   5   60   57   +   +++   2 × 2   60   51   0   +  
B   16/F   ADM   10   60   82   +   0   1 × 2   60   101   +   0  
G   50/F   ADM   14   60   56   +   +++   1 × 2   60   64   +   ++  
F   35/M   DM   3   52   302   ++   ++   2 × 2   57   103   +   0  
H   40/F   DM   2   34   1140   ++   +   7 × 2   34   344   +   0  
I   71/F   DM   < 1   25   1620   ++   ++   4 × 1   51   46   +   ++  
K   54/M   DM   3   46   343   +   0   4 × 1   45   283   0   0  
L
 
53/F
 
DM
 
< 1
 
54
 
490
 
++
 
+
 
4 × 2
 
57
 
65
 
++
 
+
 


Age, y/sex


Duration, y

Before IVIG, muscle involvement

Before IVIG, skin involvement

IVIG cycles

Final outcome, muscle involvement

Final outcome, skin involvement
Patient
Diagnosis
Score*
CK level
Extent
Pruritus
Score*
CK level
Extent
Pruritus
A   34/F   ADM   5   60   57   +   +++   2 × 2   60   51   0   +  
B   16/F   ADM   10   60   82   +   0   1 × 2   60   101   +   0  
G   50/F   ADM   14   60   56   +   +++   1 × 2   60   64   +   ++  
F   35/M   DM   3   52   302   ++   ++   2 × 2   57   103   +   0  
H   40/F   DM   2   34   1140   ++   +   7 × 2   34   344   +   0  
I   71/F   DM   < 1   25   1620   ++   ++   4 × 1   51   46   +   ++  
K   54/M   DM   3   46   343   +   0   4 × 1   45   283   0   0  
L
 
53/F
 
DM
 
< 1
 
54
 
490
 
++
 
+
 
4 × 2
 
57
 
65
 
++
 
+
 
*

Score determined according to Dalakas et al.25 

0 = none; + = localized; ++ = extensive.

0 = none; + = slight; ++ = moderate; +++ = severe.

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