Clinical features of 18 patients with LONIPCs
. | . | . | . | GVHD . | . | . | Days from SCT to LONIPCs . | PFTs at onset of LONIPCs . | . | PFTs after treatment . | . | . | . | . | . | Mo of survival from LONIPCs . | . | ||||
---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
Case no. . | LONIPC category . | Primary disease . | TBI/TLI . | Acute . | Chronic . | Sicca . | . | FVC% predicted . | FEV1/FVC . | FVC% predicted . | FEV1/FVC . | Pattern of PFTs . | Treatment outcome . | HOT . | Causes of death . | . | Alive or dead . | ||||
1 | BO | AML | − | 2 | E | + | 185 | 91.3 | 69.6 | 96.9 | 72.2 | O | PR | − | NA | 25.5 | Alive | ||||
2 | BO | AML | − | 0 | E | + | 115 | 84.2 | 69.5 | 84.6 | 65.3 | O | NC | − | NA | 74.8 | Alive | ||||
3 | BO | CML | − | 2 | E | + | 150 | 83.8 | 66.9 | ND | ND | O | P | − | Respiratory failure | 4.2 | Dead | ||||
4 | BO | MDS | − | 2 | E | + | 336 | 87.3 | 71.8 | 83.5 | 67.1 | O | P | − | P carinii pneumonia | 5.1 | Dead | ||||
5 | BO | AML | + | 2 | E | + | 94 | 105.9 | 74.5 | 59.7 | 35.4 | O | P | + | Relapse | 6.3 | Dead | ||||
6 | BO | ALL | + | 1 | E | + | 240 | 114.1 | 56.9 | 101.8 | 41.3 | O | P | + | NA | 38.8 | Alive | ||||
7 | IP | NHL | − | 0 | E | − | 180 | 120.2 | 78.3 | 116.3 | 81.1 | N | CR | − | NA | 20.4 | Alive | ||||
8 | IP | NHL | + | 2 | O | + | 204 | 121.9 | 88.0 | 111.1 | 84.5 | N | CR | − | NA | 24.5 | Alive | ||||
9 | IP | MDS | − | 1 | E | + | 1105 | 100.7 | 90.2 | 111.4 | 90.0 | N | CR | − | NA | 15.9 | Alive | ||||
10 | IP | ALL | + | 0 | O | − | 117 | 111.8 | 87.5 | 117.1 | 82.3 | N | CR | − | NA | 44.5 | Alive | ||||
11 | IP | AA | + | 3 | E | + | 140 | 112.2 | 83.4 | 126.2 | 82.8 | N | CR | − | NA | 52.3 | Alive | ||||
12 | IP | NHL | + | 0 | E | + | 91 | 96.9 | 92.3 | ND | ND | N | P | − | Respiratory failure | 1.1 | Dead | ||||
13 | IP | NHL | + | 2 | E | + | 200 | 124.8 | 81.0 | ND | ND | N | P | − | Respiratory failure | 3.1 | Dead | ||||
14 | IP | NHL | + | 1 | E | + | 300 | 54.5 | 96.4 | 30.4 | 97.8 | R | P | + | NA | 45.8 | Alive | ||||
15 | IP/BO * | AML | − | 0 | E | + | 540 | 53.1 | 57.1 | 80.3 | 69.1 | M→O | CR | − | NA | 44.0 | Alive | ||||
16 | IP | AML | + | 1 | L | + | 144 | 59.6 | 77.9 | ND | ND | R | CR | − | 2nd malignancy (MDS) | 27.4 | Dead | ||||
17 | IP | ALL | + | 2 | E | − | 153 | 65.7 | 79.9 | ND | ND | R | P | − | Respiratory failure | 1.5 | Dead | ||||
18 | IP | AML | + | 1 | E | + | 160 | 57.4 | 98.7 | 57.2 | 99.0 | R | P | + | Respiratory failure | 45.7 | Dead |
. | . | . | . | GVHD . | . | . | Days from SCT to LONIPCs . | PFTs at onset of LONIPCs . | . | PFTs after treatment . | . | . | . | . | . | Mo of survival from LONIPCs . | . | ||||
---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
Case no. . | LONIPC category . | Primary disease . | TBI/TLI . | Acute . | Chronic . | Sicca . | . | FVC% predicted . | FEV1/FVC . | FVC% predicted . | FEV1/FVC . | Pattern of PFTs . | Treatment outcome . | HOT . | Causes of death . | . | Alive or dead . | ||||
1 | BO | AML | − | 2 | E | + | 185 | 91.3 | 69.6 | 96.9 | 72.2 | O | PR | − | NA | 25.5 | Alive | ||||
2 | BO | AML | − | 0 | E | + | 115 | 84.2 | 69.5 | 84.6 | 65.3 | O | NC | − | NA | 74.8 | Alive | ||||
3 | BO | CML | − | 2 | E | + | 150 | 83.8 | 66.9 | ND | ND | O | P | − | Respiratory failure | 4.2 | Dead | ||||
4 | BO | MDS | − | 2 | E | + | 336 | 87.3 | 71.8 | 83.5 | 67.1 | O | P | − | P carinii pneumonia | 5.1 | Dead | ||||
5 | BO | AML | + | 2 | E | + | 94 | 105.9 | 74.5 | 59.7 | 35.4 | O | P | + | Relapse | 6.3 | Dead | ||||
6 | BO | ALL | + | 1 | E | + | 240 | 114.1 | 56.9 | 101.8 | 41.3 | O | P | + | NA | 38.8 | Alive | ||||
7 | IP | NHL | − | 0 | E | − | 180 | 120.2 | 78.3 | 116.3 | 81.1 | N | CR | − | NA | 20.4 | Alive | ||||
8 | IP | NHL | + | 2 | O | + | 204 | 121.9 | 88.0 | 111.1 | 84.5 | N | CR | − | NA | 24.5 | Alive | ||||
9 | IP | MDS | − | 1 | E | + | 1105 | 100.7 | 90.2 | 111.4 | 90.0 | N | CR | − | NA | 15.9 | Alive | ||||
10 | IP | ALL | + | 0 | O | − | 117 | 111.8 | 87.5 | 117.1 | 82.3 | N | CR | − | NA | 44.5 | Alive | ||||
11 | IP | AA | + | 3 | E | + | 140 | 112.2 | 83.4 | 126.2 | 82.8 | N | CR | − | NA | 52.3 | Alive | ||||
12 | IP | NHL | + | 0 | E | + | 91 | 96.9 | 92.3 | ND | ND | N | P | − | Respiratory failure | 1.1 | Dead | ||||
13 | IP | NHL | + | 2 | E | + | 200 | 124.8 | 81.0 | ND | ND | N | P | − | Respiratory failure | 3.1 | Dead | ||||
14 | IP | NHL | + | 1 | E | + | 300 | 54.5 | 96.4 | 30.4 | 97.8 | R | P | + | NA | 45.8 | Alive | ||||
15 | IP/BO * | AML | − | 0 | E | + | 540 | 53.1 | 57.1 | 80.3 | 69.1 | M→O | CR | − | NA | 44.0 | Alive | ||||
16 | IP | AML | + | 1 | L | + | 144 | 59.6 | 77.9 | ND | ND | R | CR | − | 2nd malignancy (MDS) | 27.4 | Dead | ||||
17 | IP | ALL | + | 2 | E | − | 153 | 65.7 | 79.9 | ND | ND | R | P | − | Respiratory failure | 1.5 | Dead | ||||
18 | IP | AML | + | 1 | E | + | 160 | 57.4 | 98.7 | 57.2 | 99.0 | R | P | + | Respiratory failure | 45.7 | Dead |
HOT indicates home oxygen therapy; E, extensive type; O, obstructive; PR, partial remission; NC, no change; P, progressive; N, normal; CR, complete remission; R, restrictive; M, mixed; L, limited type; NA, not applicable; and ND, not done.
Case 15: BO was diagnosed after the improvement of IP.