Main hemostatic findings of the patients studied
| Patients . | BT, min . | PTT, s . | RIPA,*% . | FVIII, U/dL . | VWF:Ag, U/dL . | VWF:RCo, U/dL . | VWF:FVIIIB, U/dL . | VWF:CB, U/dL . | Platelet VWF:Ag, U/dL . |
|---|---|---|---|---|---|---|---|---|---|
| Proband | 2 min 23 s | 39.7 | 2.5 | 39 | 51 | 45.5 | 11.9 (0.23) | 38 (0.73) | 120 |
| Father | 1 min 59 s | 39 | 21 | 48.1 | 49.3 | 35 | 22.2 (0.45) | 33.8 (0.93) | 100.5 |
| Mother | 3 min 10 s | 31.8 | 77.6 | 98 | 106 | 77 | 45.6 (0.43) | 85 (0.43) | 107.5 |
| Normal range | <4 min | 30-40 | 60-84 | 60-160 | 60-160 | 60-130 | 70-140 (>0.75) | 70-140 (>0.75) | 70-140 |
| Patients . | BT, min . | PTT, s . | RIPA,*% . | FVIII, U/dL . | VWF:Ag, U/dL . | VWF:RCo, U/dL . | VWF:FVIIIB, U/dL . | VWF:CB, U/dL . | Platelet VWF:Ag, U/dL . |
|---|---|---|---|---|---|---|---|---|---|
| Proband | 2 min 23 s | 39.7 | 2.5 | 39 | 51 | 45.5 | 11.9 (0.23) | 38 (0.73) | 120 |
| Father | 1 min 59 s | 39 | 21 | 48.1 | 49.3 | 35 | 22.2 (0.45) | 33.8 (0.93) | 100.5 |
| Mother | 3 min 10 s | 31.8 | 77.6 | 98 | 106 | 77 | 45.6 (0.43) | 85 (0.43) | 107.5 |
| Normal range | <4 min | 30-40 | 60-84 | 60-160 | 60-160 | 60-130 | 70-140 (>0.75) | 70-140 (>0.75) | 70-140 |
The values in parentheses represent the VWF:FVIIIB/VWF:Ag or VWF:CB/VWF:Ag ratios.
RIPA 1.2 mg/mL.