Table 4.

Prevalence of acquired and inherited risk factors for Budd-Chiari syndrome (BCS) and portal vein thrombosis (PVT)

Acquired risk factorInherited risk factorBCS (%)
n = 43
PVT (%)
n = 92
− − 11  (25.6) 15  (16.3)  
− 18  (41.8) 60  (65.2)  
− 8  (18.6) 4  (4.3)  
6  (13.9) 13  (14.1) 
Acquired risk factorInherited risk factorBCS (%)
n = 43
PVT (%)
n = 92
− − 11  (25.6) 15  (16.3)  
− 18  (41.8) 60  (65.2)  
− 8  (18.6) 4  (4.3)  
6  (13.9) 13  (14.1) 

BCS: Inherited risk factor: factor V Leiden mutation n = 11, prothrombin gene mutation n = 2, protein C deficiency n = 4. Acquired risk factor: oral contraceptives n = 12, myeloproliferative disease n = 12, lupus anticoagulant n = 2, inflammatory bowel disease n = 2, liver abscess n = 1.

PVT: Inherited risk factor: factor V Leiden mutation n = 7, prothrombin gene mutation n = 3, protein C deficiency n = 6, protein S deficiency n = 2, antithrombin deficiency n = 1. Acquired risk factor: oral contraceptives n = 12, myeloproliferative disease n = 16, cirrhosis n = 16, abdominal surgery n = 28, pancreatitis n = 10, umbilical vein infection n = 6, inflammatory bowel disease n = 4, liver abscess n = 4, abdominal trauma n = 2, paroxysmal nocturnal hemoglobinuria n = 2, pregnancy n = 2, nodular regenerative hyperplasia n = 2, portal sclerosis n = 1, hepatocellular carcinoma n = 1, seminoma n = 1.

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