Patient and disease characteristics and pretransplant complications
| Patient . | Age/sex . | Diagnosis . | Lymphocytes/mm3 . | PHA stimulation S.I. (normal > 100) . | Complications . | Donor . |
|---|---|---|---|---|---|---|
| 1 | 10 y/M | CID | Abs. L 180 | 6.1 | Bronchiectasis | MUD |
| CD3 81 | Sclerosing cholangitis | |||||
| CD4 61 | ||||||
| CD19 18 | ||||||
| CD16 10.8 | ||||||
| 2 | 18 y/M | CD40L deficiency | Abs. L 1470 | 361.4 | Sclerosing cholangitis | MUD |
| CD3 975 | Orthotopic liver transplantation | |||||
| CD4 780 | ||||||
| CD19 397 | ||||||
| CD16 59 | ||||||
| 3 | 11 y/M | CD40L deficiency | Abs. L 3640 | 220.7 | Sclerosing cholangitis | MUD |
| CD3 2802 | Cryptosporidiosis | |||||
| CD4 1783 | ||||||
| CD19 510 | ||||||
| CD16 218 | ||||||
| 4 | 3.8 y/M | XLP/HLH | Abs. L 1990 | 197.2 | Pneumonitis | MSD |
| CD3 1444 | CNS HLH | |||||
| CD4 896 | ||||||
| CD19 438 | ||||||
| CD16 20 | ||||||
| 5 | 9 mo/F | ADA deficiency | Abs. L 630 | 1.1 | Pneumonitis | MUD |
| CD3 170 | Enteropathy | |||||
| CD4 151 | ||||||
| CD19 12 | ||||||
| CD16 384 | ||||||
| 6 | 11 mo/M | T+B−NK− | Abs. L 1020 | 445.4 | Pneumocystis carinii pneumonitis | MUD |
| SCID | CD3 979 | |||||
| CD4 765 | Enteropathy | |||||
| CD19 30 | ||||||
| CD16 0 | ||||||
| 7 | 14 mo/M | T_B+NK− | Abs. L 1430 | 8.9 | Meningoencephalitis | MUD |
| SCID | CD3 229 | RSV bronchiolitis | ||||
| CD4 57 | Failure to thrive | |||||
| CD19 1158 | Enteropathy | |||||
| CD16 10 | ||||||
| 8 | 10 y/M | CID | Abs. L 1070 | 47.3 | Autoimmune thrombocytopenia | MSD |
| CD3 963 | ||||||
| CD4 460 | Hepatitis B infection | |||||
| CD19 0 | Enteropathy | |||||
| CD16 64 |
| Patient . | Age/sex . | Diagnosis . | Lymphocytes/mm3 . | PHA stimulation S.I. (normal > 100) . | Complications . | Donor . |
|---|---|---|---|---|---|---|
| 1 | 10 y/M | CID | Abs. L 180 | 6.1 | Bronchiectasis | MUD |
| CD3 81 | Sclerosing cholangitis | |||||
| CD4 61 | ||||||
| CD19 18 | ||||||
| CD16 10.8 | ||||||
| 2 | 18 y/M | CD40L deficiency | Abs. L 1470 | 361.4 | Sclerosing cholangitis | MUD |
| CD3 975 | Orthotopic liver transplantation | |||||
| CD4 780 | ||||||
| CD19 397 | ||||||
| CD16 59 | ||||||
| 3 | 11 y/M | CD40L deficiency | Abs. L 3640 | 220.7 | Sclerosing cholangitis | MUD |
| CD3 2802 | Cryptosporidiosis | |||||
| CD4 1783 | ||||||
| CD19 510 | ||||||
| CD16 218 | ||||||
| 4 | 3.8 y/M | XLP/HLH | Abs. L 1990 | 197.2 | Pneumonitis | MSD |
| CD3 1444 | CNS HLH | |||||
| CD4 896 | ||||||
| CD19 438 | ||||||
| CD16 20 | ||||||
| 5 | 9 mo/F | ADA deficiency | Abs. L 630 | 1.1 | Pneumonitis | MUD |
| CD3 170 | Enteropathy | |||||
| CD4 151 | ||||||
| CD19 12 | ||||||
| CD16 384 | ||||||
| 6 | 11 mo/M | T+B−NK− | Abs. L 1020 | 445.4 | Pneumocystis carinii pneumonitis | MUD |
| SCID | CD3 979 | |||||
| CD4 765 | Enteropathy | |||||
| CD19 30 | ||||||
| CD16 0 | ||||||
| 7 | 14 mo/M | T_B+NK− | Abs. L 1430 | 8.9 | Meningoencephalitis | MUD |
| SCID | CD3 229 | RSV bronchiolitis | ||||
| CD4 57 | Failure to thrive | |||||
| CD19 1158 | Enteropathy | |||||
| CD16 10 | ||||||
| 8 | 10 y/M | CID | Abs. L 1070 | 47.3 | Autoimmune thrombocytopenia | MSD |
| CD3 963 | ||||||
| CD4 460 | Hepatitis B infection | |||||
| CD19 0 | Enteropathy | |||||
| CD16 64 |