Table 2.
Routine biologic data and DNA analyses of patients
Patients
.
Bleeding Time (min)
.
FVIII:Ag (U/dL)
.
FVIII:C (U/dL)
.
vWF:Ag (U/dL)
.
vWF:RCo (U/dL)
.
Mutations
.
1
> 20
4
1.5
23
20
Cys25Tyr/(c)93Ter
2
8
30
26
65
64
Cys25Tyr/Arg91Gln
3
4
44
30
100
90
Cys95Phe/Arg91Gln
Normal
< 10
50-150
50-150
50-175
50-150
Patients
.
Bleeding Time (min)
.
FVIII:Ag (U/dL)
.
FVIII:C (U/dL)
.
vWF:Ag (U/dL)
.
vWF:RCo (U/dL)
.
Mutations
.
1
> 20
4
1.5
23
20
Cys25Tyr/(c)93Ter
2
8
30
26
65
64
Cys25Tyr/Arg91Gln
3
4
44
30
100
90
Cys95Phe/Arg91Gln
Normal
< 10
50-150
50-150
50-175
50-150
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