Leukocyte Chimerism in 22 Patients With B+SCID After BMT
| . | UPN . | Molecular Deficiency . | Age at BMT (mos) . | Follow-Up (yrs) . | CR . | Chimerism . | |||
|---|---|---|---|---|---|---|---|---|---|
| T Cells . | B Cells . | Monocytes . | NK Cells . | ||||||
| HLA-identical BMT | 17 | γc | 1 | 23 | No | D | H | H | (−) |
| 116* | γc | 1 | 13 | No | D | H | H | D | |
| 261 | γc | 6.5 | 5.5 | No | D | H | H | ND | |
| 50 | Unknown | 4.5 | 13.5 | No | D | D/H | H | D | |
| 299 | Unknown | 10 | 4.5 | No | D | H | H | H | |
| HLA-nonidentical BMT | 51* | γc | 2.5 | 13 | No | D | H | H | ND |
| 122 | γc | 6.5 | 10 | No | D | D | D | ND | |
| 307 | γc | 93 | 3.5 | No | D | H | H | (−) | |
| 325 | γc | 14 | 3 | No | D | H | H | D | |
| 277 | γc | 8 | 4.5 | No | D | H | H | ND | |
| 57 | JAK3 | 9 | 13 | No | D | H | H | (−) | |
| 223 | JAK3 | 11 | 6.5 | No | D | D | D | ND | |
| 365 | JAK3 | 5 | 2 | No | D | H | H | D | |
| 168 | γc | 2 | 8.5 | Yes | D | H | H | ND | |
| 272b | γc | 29 | 3 | Yes | D | H | H | D | |
| 303 | γc | 1 | 4 | Yes | D | H | H | D | |
| 308 | γc | 8.5 | 3.5 | Yes | D | H | H | ND | |
| 318 | γc | 5.5 | 3 | Yes | D | H | H | ND | |
| 348 | γc | 1 | 2 | Yes | D | H | H | D | |
| 158 | Unknown | 4 | 9 | Yes | D | H | H | D | |
| 360 | Unknown | 10 | 2 | Yes | D | H | H | D | |
| 221 | JAK3 | 11 | 6.5 | Yes | D | D | D | D | |
| . | UPN . | Molecular Deficiency . | Age at BMT (mos) . | Follow-Up (yrs) . | CR . | Chimerism . | |||
|---|---|---|---|---|---|---|---|---|---|
| T Cells . | B Cells . | Monocytes . | NK Cells . | ||||||
| HLA-identical BMT | 17 | γc | 1 | 23 | No | D | H | H | (−) |
| 116* | γc | 1 | 13 | No | D | H | H | D | |
| 261 | γc | 6.5 | 5.5 | No | D | H | H | ND | |
| 50 | Unknown | 4.5 | 13.5 | No | D | D/H | H | D | |
| 299 | Unknown | 10 | 4.5 | No | D | H | H | H | |
| HLA-nonidentical BMT | 51* | γc | 2.5 | 13 | No | D | H | H | ND |
| 122 | γc | 6.5 | 10 | No | D | D | D | ND | |
| 307 | γc | 93 | 3.5 | No | D | H | H | (−) | |
| 325 | γc | 14 | 3 | No | D | H | H | D | |
| 277 | γc | 8 | 4.5 | No | D | H | H | ND | |
| 57 | JAK3 | 9 | 13 | No | D | H | H | (−) | |
| 223 | JAK3 | 11 | 6.5 | No | D | D | D | ND | |
| 365 | JAK3 | 5 | 2 | No | D | H | H | D | |
| 168 | γc | 2 | 8.5 | Yes | D | H | H | ND | |
| 272b | γc | 29 | 3 | Yes | D | H | H | D | |
| 303 | γc | 1 | 4 | Yes | D | H | H | D | |
| 308 | γc | 8.5 | 3.5 | Yes | D | H | H | ND | |
| 318 | γc | 5.5 | 3 | Yes | D | H | H | ND | |
| 348 | γc | 1 | 2 | Yes | D | H | H | D | |
| 158 | Unknown | 4 | 9 | Yes | D | H | H | D | |
| 360 | Unknown | 10 | 2 | Yes | D | H | H | D | |
| 221 | JAK3 | 11 | 6.5 | Yes | D | D | D | D | |
Abbreviations: H, cells of host origin; D, cells of donor origin; ND, not done; (−), cells not found.
These 2 patients had the same γc gene mutation.