Evolution of the Lymphoproliferative Syndrome
Patient No. . | . | Age Range (yrs) . | Age at Last Follow-Up (yrs) . | ||||
---|---|---|---|---|---|---|---|
0-5 . | 5-10 . | 10-15 . | 15-20 . | >20 . | |||
2 | Lymphadenopathy | +++ | ++ | + | 0 | 15 | |
Splenomegaly | + | 0 | 0 | 0 | |||
6 | Lymphadenopathy | 0 | + | + | 13 | ||
Splenomegaly | ++ | ++ | ++ | ||||
8 | Lymphadenopathy | NE | ++ | + | 0 | 1 (5 cm × 5 cm) | 24 |
Splenomegaly | NE | +++ | 12 yrs3-150 | (axillar) | |||
9 | Lymphadenopathy | +++ | +++ | +++ | ++/+ | Accessory | 35 |
Splenomegaly | +++ | +++ | +++ | 16 yrs3-150 | Spleen | ||
11 | Lymphadenopathy | NE | 0 | +++ | ++/+ | 19 | |
Splenomegaly | NE | ++ | 10 yrs3-150 | ||||
12b | Lymphadenopathy | NE | NE | +++ | + | 0 | 25 |
Splenomegaly | NE | NE | +14 yrs3-150 | ||||
14 | Lymphadenopathy | ++ | + | 0 | 15 | ||
Splenomegaly | +++ | +++ | +++ |
Patient No. . | . | Age Range (yrs) . | Age at Last Follow-Up (yrs) . | ||||
---|---|---|---|---|---|---|---|
0-5 . | 5-10 . | 10-15 . | 15-20 . | >20 . | |||
2 | Lymphadenopathy | +++ | ++ | + | 0 | 15 | |
Splenomegaly | + | 0 | 0 | 0 | |||
6 | Lymphadenopathy | 0 | + | + | 13 | ||
Splenomegaly | ++ | ++ | ++ | ||||
8 | Lymphadenopathy | NE | ++ | + | 0 | 1 (5 cm × 5 cm) | 24 |
Splenomegaly | NE | +++ | 12 yrs3-150 | (axillar) | |||
9 | Lymphadenopathy | +++ | +++ | +++ | ++/+ | Accessory | 35 |
Splenomegaly | +++ | +++ | +++ | 16 yrs3-150 | Spleen | ||
11 | Lymphadenopathy | NE | 0 | +++ | ++/+ | 19 | |
Splenomegaly | NE | ++ | 10 yrs3-150 | ||||
12b | Lymphadenopathy | NE | NE | +++ | + | 0 | 25 |
Splenomegaly | NE | NE | +14 yrs3-150 | ||||
14 | Lymphadenopathy | ++ | + | 0 | 15 | ||
Splenomegaly | +++ | +++ | +++ |
Lymphadenopathy: 0, absence; +, multiple nodes <2 cm; ++, multiple nodes >2 cm and <5 cm; +++, multiple nodes >5 cm. Splenomegaly: +, above the umbilicus; ++, below the umbilicus; +++, palpable in the iliac fossa.
Abbreviation: NE, not evaluated.
Age at splenectomy.