Clinical Characteristics of Patients
| Patient no. | 21 | 7 |
| Age at onset of neutropenia | <1 yr | 0.5-15 yr |
| ANC at diagnosis | <500/μL | 0-1,200/μL |
| Infections | Mild | Mild-moderate |
| Associated disease | None | Evans syndrome (n = 3) |
| AIHA, ITP, IDDM (n = 1) | ||
| AIHA and CID (n = 1) | ||
| ITP (n = 1) | ||
| AI-thyroiditis (n = 1) | ||
| Spontaneous recovery ANC | Yes (n = 18) Follow-up <2 yr (n = 2) No recovery after 6 years (n = 1) | No (n = 7) |
| Diagnosis | Primary AIN | Secondary AIN |
| Patient no. | 21 | 7 |
| Age at onset of neutropenia | <1 yr | 0.5-15 yr |
| ANC at diagnosis | <500/μL | 0-1,200/μL |
| Infections | Mild | Mild-moderate |
| Associated disease | None | Evans syndrome (n = 3) |
| AIHA, ITP, IDDM (n = 1) | ||
| AIHA and CID (n = 1) | ||
| ITP (n = 1) | ||
| AI-thyroiditis (n = 1) | ||
| Spontaneous recovery ANC | Yes (n = 18) Follow-up <2 yr (n = 2) No recovery after 6 years (n = 1) | No (n = 7) |
| Diagnosis | Primary AIN | Secondary AIN |
Abbreviations: AIHA, autoimmune hemolytic anemia; ITP, immune thrombocytopenic purpura; IDDM, insulin-dependent diabetes mellitus; CID, combined immune deficiency; AI, autoimmune.