vWF Multimeric Pattern and vWF-Cleaving Protease in Patients With Recurrent HUS/TTP
| Patient (sex/age [yr]) . | Lmw vWF Multimers . | Hmw vWF Multimers . | vWF-Cleaving Protease Activity . | |||
|---|---|---|---|---|---|---|
| Acute Phase . | Remission . | Acute Phase . | Remission . | Acute Phase . | Remission . | |
| R1 (F/35) | Increased | Normal | Ultralarge | Ultralarge | 0* | 0* |
| R2 (F/3) | — | Normal | — | Ultralarge | — | 0 |
| R7 (M/18) | Increased | Normal | Decreased | Normal | — | 100% |
| R12 (M/29) | Increased | Normal | Ultralarge | Ultralarge | 0* | 0* |
| R13 (M/46) | Increased | Normal | Ultralarge | Ultralarge | — | 100% |
| R14 (M/53) | Increased | Normal | Ultralarge | Ultralarge | 0* | 0* |
| R15 (M/53) | — | Normal | — | Ultralarge | — | 100% |
| R19 (M/16) | — | Normal | — | Ultralarge | — | 0 |
| R20 (F/20) | — | Normal | — | Ultralarge | — | 20% |
| R29 (F/41) | Increased | — | Decreased | — | 0* | — |
| Patient (sex/age [yr]) . | Lmw vWF Multimers . | Hmw vWF Multimers . | vWF-Cleaving Protease Activity . | |||
|---|---|---|---|---|---|---|
| Acute Phase . | Remission . | Acute Phase . | Remission . | Acute Phase . | Remission . | |
| R1 (F/35) | Increased | Normal | Ultralarge | Ultralarge | 0* | 0* |
| R2 (F/3) | — | Normal | — | Ultralarge | — | 0 |
| R7 (M/18) | Increased | Normal | Decreased | Normal | — | 100% |
| R12 (M/29) | Increased | Normal | Ultralarge | Ultralarge | 0* | 0* |
| R13 (M/46) | Increased | Normal | Ultralarge | Ultralarge | — | 100% |
| R14 (M/53) | Increased | Normal | Ultralarge | Ultralarge | 0* | 0* |
| R15 (M/53) | — | Normal | — | Ultralarge | — | 100% |
| R19 (M/16) | — | Normal | — | Ultralarge | — | 0 |
| R20 (F/20) | — | Normal | — | Ultralarge | — | 20% |
| R29 (F/41) | Increased | — | Decreased | — | 0* | — |
Data included in study by Furlan et al.20