N-Terminal Amino Acid Sequence Analysis of the Purified ACA Cofactors
| Molecular Weight (initial yield) . | Sequence Determined* (position−) . | Sequence Expected (protein identity and species) . | Accession (SWISS-PROT) . |
|---|---|---|---|
| Patient no. 4 | |||
| 61 kD (5 pmol) | 26-ANPGLV[VS]RI | ANPGLVARI (human LBP) | P18428 |
| 61 kD (5 pmol) | SALYSS[VS]DP | Unassigned | |
| Patient no. 5 | |||
| 80 kD (7 pmol) | 49-SCGIPPYLDFAFPINEL | SCGIPPYLDFAFPINEL (bovine C4BP α chain) | Q28065 |
| Patient no. 6 | |||
| 80 kD (10 pmol) | 1-HRSPVED | HRSPVED (bovine antithrombin) | P41361 |
| 80 kD (10 pmol) | 367-IVEGQDA† | IVEGQDA (bovine thrombin B chain) | P00735 |
| 50 kD (5 pmol) | 1-HRSPVED | HRSPVED (bovine antithrombin) | P41361 |
| 33 kD (7 pmol) | 367-IVEGQDA† | IVEGQDA (bovine thrombin B chain) | P00735 |
| Molecular Weight (initial yield) . | Sequence Determined* (position−) . | Sequence Expected (protein identity and species) . | Accession (SWISS-PROT) . |
|---|---|---|---|
| Patient no. 4 | |||
| 61 kD (5 pmol) | 26-ANPGLV[VS]RI | ANPGLVARI (human LBP) | P18428 |
| 61 kD (5 pmol) | SALYSS[VS]DP | Unassigned | |
| Patient no. 5 | |||
| 80 kD (7 pmol) | 49-SCGIPPYLDFAFPINEL | SCGIPPYLDFAFPINEL (bovine C4BP α chain) | Q28065 |
| Patient no. 6 | |||
| 80 kD (10 pmol) | 1-HRSPVED | HRSPVED (bovine antithrombin) | P41361 |
| 80 kD (10 pmol) | 367-IVEGQDA† | IVEGQDA (bovine thrombin B chain) | P00735 |
| 50 kD (5 pmol) | 1-HRSPVED | HRSPVED (bovine antithrombin) | P41361 |
| 33 kD (7 pmol) | 367-IVEGQDA† | IVEGQDA (bovine thrombin B chain) | P00735 |