Clinical Data of the Patients Included in This Study
. | Age/Sex . | Disease . | Type of BMT . | Plasma Exchange . | Cyclosporin Treatment . | Result of Treatment . | Survival Time (mo) . | LDH (U/L) . | Creatinin (μmol/L) . | Hb (mmol/L) . | Platelets (×109/L) . | CellularFibronectin (ng/mL) . | vWF:Ag (%) . | vWF:RiCof (%) . |
---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
Primary TTP Patients | ||||||||||||||
1 | 43/F | Yes | Good | 22 | 1,311 | 62 | 5, 1 | 16 | 2,943 | 81 | 53 | |||
2 | 25/F | Yes | Good | 39 | 1,482 | 76 | 6, 4 | 5 | 2,221 | 88 | 71 | |||
3 | 35/F | Yes | Good | 44 | 2,086 | 188 | 6, 1 | 44 | 2,331 | 129 | 67 | |||
4 | 29/F | Yes | Good | 4 | 4,901 | 75 | 2, 9 | 11 | 3,219 | 196 | 132 | |||
5 | 29/F | Yes | Good | 4 | 1,777 | 86 | 5, 2 | 30 | 1,988 | 82 | 47 | |||
BMT-Associated TTP Patients | ||||||||||||||
6 | 57/M | MM | Autologous | Started | Good | 50 | 658 | 121 | 4, 1 | 64 | 5,153 | 261 | 137 | |
7 | 40/M | Hodgkin’s | Autologous | Started | Good | 59 | 768 | 155 | 5, 0 | 49 | 2,932 | 181 | 104 | |
8 | 52/F | NHL | Autologous | Yes* | Started | On dialysis | 72 | 1,276 | 152 | 4, 6 | 24 | 2,244 | 263 | 185 |
9 | 16/M | NHL | Autologous | Yes* | Started | Good | 56 | 999 | 201 | 4, 6 | 44 | 1,825 | 148 | 90 |
10 | 37/F | ALL | Allogeneic | Stopped | Good† | 2 | 1,016 | 86 | 5, 9 | 17 | 2,212 | 320 | 238 | |
11 | 49/F | MDS | Allogeneic | Yes* | † | 1 | 1,959 | 209 | 5, 3 | 43 | 5,275 | 485 | 125 | |
12 | 35/M | ALL | Allogeneic | Stopped | Good† | 17 | 3,570 | 345 | 5, 5 | 19 | 3,444 | 470 | 243 | |
13 | 53/M | AA | Allogeneic | Stopped | Good† | 1 | 4,300 | 210 | 5, 0 | 5 | 3,010 | 620 | 300 |
. | Age/Sex . | Disease . | Type of BMT . | Plasma Exchange . | Cyclosporin Treatment . | Result of Treatment . | Survival Time (mo) . | LDH (U/L) . | Creatinin (μmol/L) . | Hb (mmol/L) . | Platelets (×109/L) . | CellularFibronectin (ng/mL) . | vWF:Ag (%) . | vWF:RiCof (%) . |
---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
Primary TTP Patients | ||||||||||||||
1 | 43/F | Yes | Good | 22 | 1,311 | 62 | 5, 1 | 16 | 2,943 | 81 | 53 | |||
2 | 25/F | Yes | Good | 39 | 1,482 | 76 | 6, 4 | 5 | 2,221 | 88 | 71 | |||
3 | 35/F | Yes | Good | 44 | 2,086 | 188 | 6, 1 | 44 | 2,331 | 129 | 67 | |||
4 | 29/F | Yes | Good | 4 | 4,901 | 75 | 2, 9 | 11 | 3,219 | 196 | 132 | |||
5 | 29/F | Yes | Good | 4 | 1,777 | 86 | 5, 2 | 30 | 1,988 | 82 | 47 | |||
BMT-Associated TTP Patients | ||||||||||||||
6 | 57/M | MM | Autologous | Started | Good | 50 | 658 | 121 | 4, 1 | 64 | 5,153 | 261 | 137 | |
7 | 40/M | Hodgkin’s | Autologous | Started | Good | 59 | 768 | 155 | 5, 0 | 49 | 2,932 | 181 | 104 | |
8 | 52/F | NHL | Autologous | Yes* | Started | On dialysis | 72 | 1,276 | 152 | 4, 6 | 24 | 2,244 | 263 | 185 |
9 | 16/M | NHL | Autologous | Yes* | Started | Good | 56 | 999 | 201 | 4, 6 | 44 | 1,825 | 148 | 90 |
10 | 37/F | ALL | Allogeneic | Stopped | Good† | 2 | 1,016 | 86 | 5, 9 | 17 | 2,212 | 320 | 238 | |
11 | 49/F | MDS | Allogeneic | Yes* | † | 1 | 1,959 | 209 | 5, 3 | 43 | 5,275 | 485 | 125 | |
12 | 35/M | ALL | Allogeneic | Stopped | Good† | 17 | 3,570 | 345 | 5, 5 | 19 | 3,444 | 470 | 243 | |
13 | 53/M | AA | Allogeneic | Stopped | Good† | 1 | 4,300 | 210 | 5, 0 | 5 | 3,010 | 620 | 300 |