Table 1. Clinical Characteristics .... | American Society of Hematology

Table 1.

Clinical Characteristics

	Cases
	1	2	3	4	5	6	7
Age of onset (erythroderma)	2 mo	2 mo	2 wk	4 mo	4 mo	2 mo	2 wk
Facial anomalies	+	−	−	+++	−	−	−
Thymic abnormalities	+++	na^*	++	+++	na	na	++
Erythroderma/exfoliative dermatitis	++	++	+	+++	+	+	+
Hepatomegaly	++	++	++	++	+++	++	+
Lymphadenopathy	++	++	++	+++	+++	++	+
Diarrhea	++	++	++	++	++	+++	++
Failure to thrive	+	++	+	+++	++	+++	+
Pulmonary edema	++	−	−	++	−	−	−
Lymphocytosis	+	nl	nl	+++	nl	++	+
Eosinophilia	+	+	++	++	nl	+	+
IgG	nl	dec	dec	dec	dec	dec	nl
IgE	na	inc	inc	na	inc	inc	inc

	Cases
	1	2	3	4	5	6	7
Age of onset (erythroderma)	2 mo	2 mo	2 wk	4 mo	4 mo	2 mo	2 wk
Facial anomalies	+	−	−	+++	−	−	−
Thymic abnormalities	+++	na^*	++	+++	na	na	++
Erythroderma/exfoliative dermatitis	++	++	+	+++	+	+	+
Hepatomegaly	++	++	++	++	+++	++	+
Lymphadenopathy	++	++	++	+++	+++	++	+
Diarrhea	++	++	++	++	++	+++	++
Failure to thrive	+	++	+	+++	++	+++	+
Pulmonary edema	++	−	−	++	−	−	−
Lymphocytosis	+	nl	nl	+++	nl	++	+
Eosinophilia	+	+	++	++	nl	+	+
IgG	nl	dec	dec	dec	dec	dec	nl
IgE	na	inc	inc	na	inc	inc	inc

Abbreviations: na, not assessed; nl, normal; dec, decreased; inc, increased.