Presenting Features
| Features . | JMML (n = 60) . | A-MDS (n = 101) . | TMS (n = 6) . | Total (n = 167) . |
|---|---|---|---|---|
| Demographics3-150 | ||||
| Age in years (range) | 1.3 (0-7.6) | 8.0 (0-20.0) | 0.6 (0-0.3) | 3.2 (0-20.0) |
| Gender (M:F) | 1.7:1 | 1.2:1 | 2:1 | 1.4:1 |
| Physical findings3-151 | ||||
| Skin | 17 (28) | 7 (7) | 2 (33) | 26 (16) |
| Hepatomegaly | 45 (75) | 22 (22) | 2 (33) | 69 (41) |
| Splenomegaly | 52 (87) | 26 (26) | 3 (50) | 81 (46) |
| Adenopathy | 24 (40) | 9 (9) | 0 | 33 (20) |
| CBC3-150 | ||||
| Hg (g/dL) | 9.0 (3-13.6) | 6.0 (2.8-16.8) | 11.3 (5.7-17.7) | 7.5 (3-17.6) |
| WBC (109/μL) | 32.0 (1-767) | 3.0 (1-100) | 14.6 (5.5-66) | 6.1 (1-767) |
| Platelets (109/μL) | 39 (4-600) | 44 (5-466) | 74 (50-129) | 44 (5-600) |
| Monocytes (%) | 8 (3-45) | 0 (0-52) | 1 (0-8) | 1 (0-45) |
| HgF >10%3-152 (%) | 24/29 (83) | 3/8 (38) | NA | 27/37 (73) |
| Features . | JMML (n = 60) . | A-MDS (n = 101) . | TMS (n = 6) . | Total (n = 167) . |
|---|---|---|---|---|
| Demographics3-150 | ||||
| Age in years (range) | 1.3 (0-7.6) | 8.0 (0-20.0) | 0.6 (0-0.3) | 3.2 (0-20.0) |
| Gender (M:F) | 1.7:1 | 1.2:1 | 2:1 | 1.4:1 |
| Physical findings3-151 | ||||
| Skin | 17 (28) | 7 (7) | 2 (33) | 26 (16) |
| Hepatomegaly | 45 (75) | 22 (22) | 2 (33) | 69 (41) |
| Splenomegaly | 52 (87) | 26 (26) | 3 (50) | 81 (46) |
| Adenopathy | 24 (40) | 9 (9) | 0 | 33 (20) |
| CBC3-150 | ||||
| Hg (g/dL) | 9.0 (3-13.6) | 6.0 (2.8-16.8) | 11.3 (5.7-17.7) | 7.5 (3-17.6) |
| WBC (109/μL) | 32.0 (1-767) | 3.0 (1-100) | 14.6 (5.5-66) | 6.1 (1-767) |
| Platelets (109/μL) | 39 (4-600) | 44 (5-466) | 74 (50-129) | 44 (5-600) |
| Monocytes (%) | 8 (3-45) | 0 (0-52) | 1 (0-8) | 1 (0-45) |
| HgF >10%3-152 (%) | 24/29 (83) | 3/8 (38) | NA | 27/37 (73) |