Porphyrin Levels of the Patient Before and After BMT
| Porphyrin . | Normal . | Pre-BMT . | Days Post-BMT . | ||
|---|---|---|---|---|---|
| 122 . | 241 . | 406 . | |||
| Protoporphyrins | |||||
| Serum, μg/dL | <5 | 135 | 42.3 | — | 44.4 |
| Coproporphyrins | |||||
| Serum, μg/dL | <4.5 | 208 | 37.4 | — | 24.2 |
| Urine, μg/mL | <60 | 297 | 102 | 83.4 | — |
| Uroporphyrins | |||||
| Serum, μg/dL | <3.0 | 112 | 26.2 | — | 18.3 |
| Urine, μg/mL | <10.0 | 382 | 88.7 | 52.3 | — |
| Porphyrin . | Normal . | Pre-BMT . | Days Post-BMT . | ||
|---|---|---|---|---|---|
| 122 . | 241 . | 406 . | |||
| Protoporphyrins | |||||
| Serum, μg/dL | <5 | 135 | 42.3 | — | 44.4 |
| Coproporphyrins | |||||
| Serum, μg/dL | <4.5 | 208 | 37.4 | — | 24.2 |
| Urine, μg/mL | <60 | 297 | 102 | 83.4 | — |
| Uroporphyrins | |||||
| Serum, μg/dL | <3.0 | 112 | 26.2 | — | 18.3 |
| Urine, μg/mL | <10.0 | 382 | 88.7 | 52.3 | — |
Normal levels are for children 2 to 12 years old.36Pre-BMT, the uroporphyrins and coproporphyrins were >90% type I isomers. Post-BMT, the type I isomer content was reduced to near normal type III/I ratios.