Hematological and Clinical Results in Five Heterozygous Carriers of Hb-Oman
. | Age . | P* . | Hb g/dL . | MCV FL . | MCH pg . | RDW . | Recticulocytes % . | Spleen . | α Gene . | S-Oman % . | HbF % . |
---|---|---|---|---|---|---|---|---|---|---|---|
HSR | 18 | ++ | 9 | 75.7 | 25 | 23.4 | 4.9 | + | −α/αα | 22.3 | 1.65 |
MSR | 11 | + | 8.3 | 69.0 | 23.2 | 29.2 | 5.4 | ++ | −α/αα | 19.7 | 4.6 |
ISH | 6 | ++ | 9.9 | 70 | 23.2 | 17.9 | 1.9 | − | −α/αα | 19.8 | 2.2 |
SSR | 37 | − | 13.8 | 66.3 | 21.7 | 13.9 | 1.3 | − | −α/−α | 14.7 | 0.76 |
MSK | 40 | − | 11 | 66.8 | 21.4 | 15.8 | 1.1 | − | −α/−α | 12.6 | 0.73 |
. | Age . | P* . | Hb g/dL . | MCV FL . | MCH pg . | RDW . | Recticulocytes % . | Spleen . | α Gene . | S-Oman % . | HbF % . |
---|---|---|---|---|---|---|---|---|---|---|---|
HSR | 18 | ++ | 9 | 75.7 | 25 | 23.4 | 4.9 | + | −α/αα | 22.3 | 1.65 |
MSR | 11 | + | 8.3 | 69.0 | 23.2 | 29.2 | 5.4 | ++ | −α/αα | 19.7 | 4.6 |
ISH | 6 | ++ | 9.9 | 70 | 23.2 | 17.9 | 1.9 | − | −α/αα | 19.8 | 2.2 |
SSR | 37 | − | 13.8 | 66.3 | 21.7 | 13.9 | 1.3 | − | −α/−α | 14.7 | 0.76 |
MSK | 40 | − | 11 | 66.8 | 21.4 | 15.8 | 1.1 | − | −α/−α | 12.6 | 0.73 |
Clinical phenotype.