Clinical Characteristics of Patients
| . | Age/Sex . | Duration SS . | Anti–SS-A/SS-B . | RF . | Cryo . | Mono Ig . | Hypo Ig . | Localization . | Treatment . | Response (yr) . |
|---|---|---|---|---|---|---|---|---|---|---|
| 1 | 80/F | 25 | Yes | Yes | Yes | Mk | Yes | Buccal mucosa | CLB | CR (2) |
| Lymph node | ||||||||||
| Lung | ||||||||||
| 2 | 63/M | 12 | Yes | No | No | No | No | Stomach | ACVBP | CR (1) |
| MTX | ||||||||||
| 3 | 57/F | 12 | Yes | Yes | No | No | No | Parotid | CPM | CR (5) |
| Peripheral nerve | ||||||||||
| 4 | 18/F | 4 | Yes | Yes | No | No | No | Parotid | CLB | CR (5) |
| Skin | ||||||||||
| 5 | 60/M | 18 | No | No | No | No | Yes | Bronchus | CLB | |
| Lung | CHOP | PR (2) | ||||||||
| Lymph node | ACVBP | Relapse | ||||||||
| 6 | 38/F | 2 | Yes | No | No | No | No | Parotid | MTX | CR (1) |
| 7 | 71/M | 15 | Yes | Yes | No | No | Yes | Skin | CHOP | CR (0.5) |
| Muscle | COP | Dead | ||||||||
| 8 | 66/F | 0 | No | No | No | No | No | Parotid | mBACOD | CR (7) |
| Lymph node | ||||||||||
| 9 | 64/M | 2 | Yes | No | No | No | No | Lymph node | ACVBP | CR (8) |
| 10 | 62/M | 10 | No | Yes | No | No | No | Lymph node | COP | CR (9) |
| Radiotherapy | ||||||||||
| 11 | 38/F | 10 | Yes | Yes | No | Mk | No | Parotid | ||
| Thymus | CHOP | PR (3) | ||||||||
| Stomach | CPM | |||||||||
| 12 | 60/F | 4 | Yes | Yes | Yes | Mk | No | Lymph node | CHOP | PR (1.5) |
| Stomach | CLB | |||||||||
| 13 | 73/F | 0 | No | No | No | No | No | Stomach | CLB/IFN | PR (0.5) |
| Skin | Dead | |||||||||
| 14 | 56/F | 2 | Lymph node | COP | CR (12) | |||||
| 15 | 48/F | 11 | Yes | Yes | No | No | No | Parotid | CLB | CR (2) |
| 16 | 71/F | 22 | Yes | Yes | No | No | No | Parotid | CHOP | CR (0.5) |
| Lung |
| . | Age/Sex . | Duration SS . | Anti–SS-A/SS-B . | RF . | Cryo . | Mono Ig . | Hypo Ig . | Localization . | Treatment . | Response (yr) . |
|---|---|---|---|---|---|---|---|---|---|---|
| 1 | 80/F | 25 | Yes | Yes | Yes | Mk | Yes | Buccal mucosa | CLB | CR (2) |
| Lymph node | ||||||||||
| Lung | ||||||||||
| 2 | 63/M | 12 | Yes | No | No | No | No | Stomach | ACVBP | CR (1) |
| MTX | ||||||||||
| 3 | 57/F | 12 | Yes | Yes | No | No | No | Parotid | CPM | CR (5) |
| Peripheral nerve | ||||||||||
| 4 | 18/F | 4 | Yes | Yes | No | No | No | Parotid | CLB | CR (5) |
| Skin | ||||||||||
| 5 | 60/M | 18 | No | No | No | No | Yes | Bronchus | CLB | |
| Lung | CHOP | PR (2) | ||||||||
| Lymph node | ACVBP | Relapse | ||||||||
| 6 | 38/F | 2 | Yes | No | No | No | No | Parotid | MTX | CR (1) |
| 7 | 71/M | 15 | Yes | Yes | No | No | Yes | Skin | CHOP | CR (0.5) |
| Muscle | COP | Dead | ||||||||
| 8 | 66/F | 0 | No | No | No | No | No | Parotid | mBACOD | CR (7) |
| Lymph node | ||||||||||
| 9 | 64/M | 2 | Yes | No | No | No | No | Lymph node | ACVBP | CR (8) |
| 10 | 62/M | 10 | No | Yes | No | No | No | Lymph node | COP | CR (9) |
| Radiotherapy | ||||||||||
| 11 | 38/F | 10 | Yes | Yes | No | Mk | No | Parotid | ||
| Thymus | CHOP | PR (3) | ||||||||
| Stomach | CPM | |||||||||
| 12 | 60/F | 4 | Yes | Yes | Yes | Mk | No | Lymph node | CHOP | PR (1.5) |
| Stomach | CLB | |||||||||
| 13 | 73/F | 0 | No | No | No | No | No | Stomach | CLB/IFN | PR (0.5) |
| Skin | Dead | |||||||||
| 14 | 56/F | 2 | Lymph node | COP | CR (12) | |||||
| 15 | 48/F | 11 | Yes | Yes | No | No | No | Parotid | CLB | CR (2) |
| 16 | 71/F | 22 | Yes | Yes | No | No | No | Parotid | CHOP | CR (0.5) |
| Lung |
Abbreviations: RF, rheumatoid factor; mono Ig, monoclonal Ig; hypo Ig, hypogammaglobulinemia; CR, complete remission; PR, partial remission; CLB, chlorambucil; CPM, cyclophosphamide; MTX, methotrexate; IFN, α interferon; COP, cyclophosphamide + vincristine + prednisone; CHOP, cyclophosphamide + doxorubicine + vincristine + prednisone; CVB, cyclophosphamide + vindesine + bleomycine; ACVBP, doxorubicine + cyclophosphamide + vindesine + bleomycine + prednisone; MBACOD, methotrexate + bleomycine + doxorubicine + cyclophosphamide + vincristine + dexamethasone.