Table 1.

Baseline levels for hemophilia A carriers and control patients

Hemophilia A carriers (n=17)Normal controls (n = 7)
Median age (range), y 34 (25-60) 21* (18-45) 
Median ISTH-BAT BS (range) 8 (0-18) 0* (0-4) 
Blood type O, % 53 (n = 13) 57 (n = 7) 
Median FVIII level (range), IU/mL 0.55 (0.31-1.25) 1.20* (0.82-1.98) 
Median VWF:Ag (range), IU/mL 0.77 (0.32-1.68) 0.82 (0.55-1.35) 
Median VWF activity (range), IU/mL 0.55 (0.35-1.66) 0.67 (0.48-1.44) 
Median VWFpp:Ag ratio (range) 1.10 (0.6-1.8) (n = 8) 1.50 (1.2-1.9) (n = 5) 
Hemophilia A carriers (n=17)Normal controls (n = 7)
Median age (range), y 34 (25-60) 21* (18-45) 
Median ISTH-BAT BS (range) 8 (0-18) 0* (0-4) 
Blood type O, % 53 (n = 13) 57 (n = 7) 
Median FVIII level (range), IU/mL 0.55 (0.31-1.25) 1.20* (0.82-1.98) 
Median VWF:Ag (range), IU/mL 0.77 (0.32-1.68) 0.82 (0.55-1.35) 
Median VWF activity (range), IU/mL 0.55 (0.35-1.66) 0.67 (0.48-1.44) 
Median VWFpp:Ag ratio (range) 1.10 (0.6-1.8) (n = 8) 1.50 (1.2-1.9) (n = 5) 
*

P ≤ .01.

VWF:GPIbM or VWF:RCo.

P ≤ .05.

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