Baseline levels for hemophilia A carriers and control patients
. | Hemophilia A carriers (n=17) . | Normal controls (n = 7) . |
---|---|---|
Median age (range), y | 34 (25-60) | 21* (18-45) |
Median ISTH-BAT BS (range) | 8 (0-18) | 0* (0-4) |
Blood type O, % | 53 (n = 13) | 57 (n = 7) |
Median FVIII level (range), IU/mL | 0.55 (0.31-1.25) | 1.20* (0.82-1.98) |
Median VWF:Ag (range), IU/mL | 0.77 (0.32-1.68) | 0.82 (0.55-1.35) |
Median VWF activity (range), IU/mL† | 0.55 (0.35-1.66) | 0.67 (0.48-1.44) |
Median VWFpp:Ag ratio (range) | 1.10 (0.6-1.8) (n = 8) | 1.50‡ (1.2-1.9) (n = 5) |
. | Hemophilia A carriers (n=17) . | Normal controls (n = 7) . |
---|---|---|
Median age (range), y | 34 (25-60) | 21* (18-45) |
Median ISTH-BAT BS (range) | 8 (0-18) | 0* (0-4) |
Blood type O, % | 53 (n = 13) | 57 (n = 7) |
Median FVIII level (range), IU/mL | 0.55 (0.31-1.25) | 1.20* (0.82-1.98) |
Median VWF:Ag (range), IU/mL | 0.77 (0.32-1.68) | 0.82 (0.55-1.35) |
Median VWF activity (range), IU/mL† | 0.55 (0.35-1.66) | 0.67 (0.48-1.44) |
Median VWFpp:Ag ratio (range) | 1.10 (0.6-1.8) (n = 8) | 1.50‡ (1.2-1.9) (n = 5) |