Characteristics of PNH patients
Patient . | Sex . | Sampling time point . | Age at sampling, y . | Time after diagnosis, y . | WBC, ×109/L . | Hb, g/dL . | Platelets, ×109/L . | LDH, IU/L* . | Treatment at sampling . |
---|---|---|---|---|---|---|---|---|---|
PNH01 | Female | First | 44 | 20 | 2.4 | 9.3 | 101 | 274 | Eculizumab |
Second† | 46 | 22 | 5.3 | 9.6 | 142 | 192 | Eculizumab | ||
PNH02 | Female | First | 54 | 28 | 3.8 | 11.9 | 194 | 195 | Eculizumab |
Second‡ | 57 | 31 | 3.3 | 11.5 | 119 | 205 | Eculizumab | ||
PNH03 | Female | First | 83 | 15 | 1.6 | 10.4 | 107 | 208 | Eculizumab |
Second§ | 86 | 18 | 1.5 | 9.8 | 111 | 215 | Eculizumab | ||
PNH04 | Female | First | 63 | 3 | 6.3 | 7.1 | 41 | 168 | Cyclosporin A; eculizumab |
PNH05 | Female | First | 49 | 5 | 3.7 | 6.8 | 180 | 1898 | Metenolone; RBC transfusion |
PNH06 | Female | First | 28 | 3 | 5.5 | 10.6 | 191 | 670 | Cyclosporin A |
Patient . | Sex . | Sampling time point . | Age at sampling, y . | Time after diagnosis, y . | WBC, ×109/L . | Hb, g/dL . | Platelets, ×109/L . | LDH, IU/L* . | Treatment at sampling . |
---|---|---|---|---|---|---|---|---|---|
PNH01 | Female | First | 44 | 20 | 2.4 | 9.3 | 101 | 274 | Eculizumab |
Second† | 46 | 22 | 5.3 | 9.6 | 142 | 192 | Eculizumab | ||
PNH02 | Female | First | 54 | 28 | 3.8 | 11.9 | 194 | 195 | Eculizumab |
Second‡ | 57 | 31 | 3.3 | 11.5 | 119 | 205 | Eculizumab | ||
PNH03 | Female | First | 83 | 15 | 1.6 | 10.4 | 107 | 208 | Eculizumab |
Second§ | 86 | 18 | 1.5 | 9.8 | 111 | 215 | Eculizumab | ||
PNH04 | Female | First | 63 | 3 | 6.3 | 7.1 | 41 | 168 | Cyclosporin A; eculizumab |
PNH05 | Female | First | 49 | 5 | 3.7 | 6.8 | 180 | 1898 | Metenolone; RBC transfusion |
PNH06 | Female | First | 28 | 3 | 5.5 | 10.6 | 191 | 670 | Cyclosporin A |