Autoimmune cytopenias in common variable immune deficiency
. | USIDNET Registry8 (N = 990) . | ESID Registry2 (N = 2700) . |
---|---|---|
Any autoimmune cytopenia | 101 (10.2%) | — |
Autoimmune cytopenia in ≥2 cell lines | 38 (3.8%) | — |
Autoimmune cytopenia in 3 cell lines | 4 (0.4%) | — |
Evans syndrome | 16 (1.6%) | — |
Immune thrombocytopenia | 73 (7.4%) | 162 (6.0%) |
Hemolytic anemia | 56 (5.1%) | 110 (4.1%) |
Autoimmune neutropenia | 10 (1%) | — |
. | USIDNET Registry8 (N = 990) . | ESID Registry2 (N = 2700) . |
---|---|---|
Any autoimmune cytopenia | 101 (10.2%) | — |
Autoimmune cytopenia in ≥2 cell lines | 38 (3.8%) | — |
Autoimmune cytopenia in 3 cell lines | 4 (0.4%) | — |
Evans syndrome | 16 (1.6%) | — |
Immune thrombocytopenia | 73 (7.4%) | 162 (6.0%) |
Hemolytic anemia | 56 (5.1%) | 110 (4.1%) |
Autoimmune neutropenia | 10 (1%) | — |