Table 1.

Autoimmune cytopenias in common variable immune deficiency

USIDNET Registry (N = 990)ESID Registry (N = 2700)
Any autoimmune cytopenia 101 (10.2%) — 
Autoimmune cytopenia in ≥2 cell lines 38 (3.8%) — 
Autoimmune cytopenia in 3 cell lines 4 (0.4%) — 
Evans syndrome 16 (1.6%) — 
Immune thrombocytopenia 73 (7.4%) 162 (6.0%) 
Hemolytic anemia 56 (5.1%) 110 (4.1%) 
Autoimmune neutropenia 10 (1%) — 
USIDNET Registry (N = 990)ESID Registry (N = 2700)
Any autoimmune cytopenia 101 (10.2%) — 
Autoimmune cytopenia in ≥2 cell lines 38 (3.8%) — 
Autoimmune cytopenia in 3 cell lines 4 (0.4%) — 
Evans syndrome 16 (1.6%) — 
Immune thrombocytopenia 73 (7.4%) 162 (6.0%) 
Hemolytic anemia 56 (5.1%) 110 (4.1%) 
Autoimmune neutropenia 10 (1%) — 
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