Table 1.

Classification of sickle hepatopathy

Acute liver diseaseChronic liver disease
Related to sickling process • Acute sickle hepatic crisis
• Hepatic sequestration
• Sickle intrahepatic cholestasis 
• Chronic cholestasis
• Biliary-type cirrhosis 
Related to multiple blood transfusion • Viral hepatitis B and C • Chronic viral hepatitis
• Iron overload 
Miscellaneous • Cholelithiasis
• Budd-Chiari syndrome
• Hepatic abscess/biloma 
• Cholelithiasis
• Coincidental chronic liver disease, eg, autoimmune 
Acute liver diseaseChronic liver disease
Related to sickling process • Acute sickle hepatic crisis
• Hepatic sequestration
• Sickle intrahepatic cholestasis 
• Chronic cholestasis
• Biliary-type cirrhosis 
Related to multiple blood transfusion • Viral hepatitis B and C • Chronic viral hepatitis
• Iron overload 
Miscellaneous • Cholelithiasis
• Budd-Chiari syndrome
• Hepatic abscess/biloma 
• Cholelithiasis
• Coincidental chronic liver disease, eg, autoimmune 

Reproduced from Tavabie and Suddle with permission.

Close Modal

or Create an Account

Close Modal
Close Modal