The efficacy of DDAVP infusion in 6 F5F8D patients
Patients . | 0 h . | DDAVP infusion . | Outcome . | ||||
---|---|---|---|---|---|---|---|
0.5 h . | 1 h . | 2 h . | 4 h . | ||||
FVIII:C (IU/dL) . | FVIII:C (IU/dL) . | Increase (fold) . | FVIII:C (IU/dL) . | FVIII:C (IU/dL) . | FVIII:C (IU/dL) . | ||
P1 | 21.2 | 77.0 | 3.6 | 75.8 | 74.2 | 65.5 | CR |
P2 | 18.8 | 75.4 | 4.0 | 70.1 | 61.0 | 52.9 | CR |
P3 | 13.9 | 66.1 | 4.8 | 60.2 | 53.6 | 46.2 | CR |
P4 | 17.4 | 90.5 | 5.2 | 78.7 | 61.5 | 47.8 | CR |
P5 | 16.0 | 52.1 | 3.3 | 50.1 | 46.1 | 43.0 | CR |
P6 | 8.1 | 46.5 | 5.7 | 43.3 | 39.7 | 28.4 | PR |
Patients . | 0 h . | DDAVP infusion . | Outcome . | ||||
---|---|---|---|---|---|---|---|
0.5 h . | 1 h . | 2 h . | 4 h . | ||||
FVIII:C (IU/dL) . | FVIII:C (IU/dL) . | Increase (fold) . | FVIII:C (IU/dL) . | FVIII:C (IU/dL) . | FVIII:C (IU/dL) . | ||
P1 | 21.2 | 77.0 | 3.6 | 75.8 | 74.2 | 65.5 | CR |
P2 | 18.8 | 75.4 | 4.0 | 70.1 | 61.0 | 52.9 | CR |
P3 | 13.9 | 66.1 | 4.8 | 60.2 | 53.6 | 46.2 | CR |
P4 | 17.4 | 90.5 | 5.2 | 78.7 | 61.5 | 47.8 | CR |
P5 | 16.0 | 52.1 | 3.3 | 50.1 | 46.1 | 43.0 | CR |
P6 | 8.1 | 46.5 | 5.7 | 43.3 | 39.7 | 28.4 | PR |
CR, complete responder; PR, partial responder.