Demographics of DBAR participants
| . | Total . | STs* . | Leukemia . | MDS . | No cancer or MDS . |
|---|---|---|---|---|---|
| No. of cases | 608 | 15 | 2 | 4 (includes 1 ST and 1 AML) | 589 |
| Male-female ratio | 306:302 | 5:10 | 2:0 | 3:1 | 298:291 |
| Birth years | 1941-2009 | 1941-1987 | 1954, 1958 | 1952-2007 | 1941-2009 |
| Person-years | 9458 | 501 | 90 | 116 | ND |
| Age at diagnosis of DBA | 3 mo (birth-30 y) | 3 mo (birth-29 y) | 3 mo, unstated | 8 mo (2 mo-1 y) | 3 mo (birth-30 y) |
| Age at event or last follow-up | 18 (< 1-69) | 41 (13-64) | 44, 46 | 32 (2-50) | 18 (< 1-69) |
| No. who died | 60 | 6 | 2 | 2 | 50 |
| Age at death | 18 (1 mo-64 y) | 33 (14-64) | 45, 46 | 18, 46 | 18 (1 mo-64 y) |
| No. who had BMT | 62 | 0 | 1 | 1 | 60 |
| Age at BMT | 8 (1-45) | 45 | 2 | 8 (1-45) |
| . | Total . | STs* . | Leukemia . | MDS . | No cancer or MDS . |
|---|---|---|---|---|---|
| No. of cases | 608 | 15 | 2 | 4 (includes 1 ST and 1 AML) | 589 |
| Male-female ratio | 306:302 | 5:10 | 2:0 | 3:1 | 298:291 |
| Birth years | 1941-2009 | 1941-1987 | 1954, 1958 | 1952-2007 | 1941-2009 |
| Person-years | 9458 | 501 | 90 | 116 | ND |
| Age at diagnosis of DBA | 3 mo (birth-30 y) | 3 mo (birth-29 y) | 3 mo, unstated | 8 mo (2 mo-1 y) | 3 mo (birth-30 y) |
| Age at event or last follow-up | 18 (< 1-69) | 41 (13-64) | 44, 46 | 32 (2-50) | 18 (< 1-69) |
| No. who died | 60 | 6 | 2 | 2 | 50 |
| Age at death | 18 (1 mo-64 y) | 33 (14-64) | 45, 46 | 18, 46 | 18 (1 mo-64 y) |
| No. who had BMT | 62 | 0 | 1 | 1 | 60 |
| Age at BMT | 8 (1-45) | 45 | 2 | 8 (1-45) |
All ages are median (range) in years unless otherwise stated.
DBA indicates Diamond Blackfan anemia; DBAR, Diamond Blackfan Anemia Registry; ND, not done; and BMT, bone marrow (stem cell) transplantation.
STs in patients who had not received a BMT.