Patient, disease and transplant characteristics
| . | Primary disease . | All diseases, n (%)* . | |
|---|---|---|---|
| HLH, n (%)* . | Other PID, n (%)* . | ||
| Age, y | |||
| <1 | 13 (38) | 1 (8) | 14 (30) |
| 1-9 | 13 (38) | 7 (58) | 20 (43) |
| 10-19 | 7 (21) | 2 (17) | 9 (20) |
| 20-29 | 1 (3) | 2 (17) | 3 (7) |
| Sex | |||
| Female | 11 (32) | 4 (33) | 15 (33) |
| Male | 23 (68) | 8 (67) | 31 (67) |
| Race | |||
| Caucasian | 26 (76) | 9 (75) | 35 (76) |
| African American | 4 (12) | 2 (17) | 6 (13) |
| Asian | 2 (6) | 0 (0) | 2 (4) |
| Not reported | 2 (6) | 1 (8) | 3 (7) |
| Performance score | |||
| 90-100 | 24 (70) | 10 (83) | 34 (74) |
| 80 | 6 (18) | 2 (17) | 8 (17) |
| 70 | 2 (6) | 0 (0) | 2 (4) |
| 60 | 1 (3) | 0 (0) | 1 (2) |
| 50 | 1 (3) | 0 (0) | 1 (2) |
| Disease type | |||
| Hemophagocytic lymphohistiocytosis | 34 (100) | 0 (0) | 34 (74) |
| Chronic active Epstein-Barr virus | 0 (0) | 3 (25) | 3 (7) |
| Chronic granulomatous disease | 0 (0) | 5 (42) | 5 (11) |
| HIGM1 syndrome | 0 (0) | 2 (17) | 2 (4) |
| IPEX | 0 (0) | 2 (17) | 2 (4) |
| Donor type | |||
| HLA-matched sibling | 7 (21) | 0 (0) | 7 (16) |
| 1 HLA locus mismatched relative | 0 (0) | 1 (8) | 1 (2) |
| HLA matched unrelated donor | 16 (47) | 9 (75) | 25 (54) |
| 1 HLA locus mismatched unrelated donor | 11 (32) | 2 (17) | 13 (28) |
| . | Primary disease . | All diseases, n (%)* . | |
|---|---|---|---|
| HLH, n (%)* . | Other PID, n (%)* . | ||
| Age, y | |||
| <1 | 13 (38) | 1 (8) | 14 (30) |
| 1-9 | 13 (38) | 7 (58) | 20 (43) |
| 10-19 | 7 (21) | 2 (17) | 9 (20) |
| 20-29 | 1 (3) | 2 (17) | 3 (7) |
| Sex | |||
| Female | 11 (32) | 4 (33) | 15 (33) |
| Male | 23 (68) | 8 (67) | 31 (67) |
| Race | |||
| Caucasian | 26 (76) | 9 (75) | 35 (76) |
| African American | 4 (12) | 2 (17) | 6 (13) |
| Asian | 2 (6) | 0 (0) | 2 (4) |
| Not reported | 2 (6) | 1 (8) | 3 (7) |
| Performance score | |||
| 90-100 | 24 (70) | 10 (83) | 34 (74) |
| 80 | 6 (18) | 2 (17) | 8 (17) |
| 70 | 2 (6) | 0 (0) | 2 (4) |
| 60 | 1 (3) | 0 (0) | 1 (2) |
| 50 | 1 (3) | 0 (0) | 1 (2) |
| Disease type | |||
| Hemophagocytic lymphohistiocytosis | 34 (100) | 0 (0) | 34 (74) |
| Chronic active Epstein-Barr virus | 0 (0) | 3 (25) | 3 (7) |
| Chronic granulomatous disease | 0 (0) | 5 (42) | 5 (11) |
| HIGM1 syndrome | 0 (0) | 2 (17) | 2 (4) |
| IPEX | 0 (0) | 2 (17) | 2 (4) |
| Donor type | |||
| HLA-matched sibling | 7 (21) | 0 (0) | 7 (16) |
| 1 HLA locus mismatched relative | 0 (0) | 1 (8) | 1 (2) |
| HLA matched unrelated donor | 16 (47) | 9 (75) | 25 (54) |
| 1 HLA locus mismatched unrelated donor | 11 (32) | 2 (17) | 13 (28) |
Column percentage given.