Long-term assessment of patients with ALPS-related symptoms present < 15 years and with a follow-up of > 20 years (N = 42)
| Less than 15 years, n (%)* . | More than 20 years, n (%)† . | |
|---|---|---|
| Lymphoproliferation 42 (100) | Complete remission | 28 (66) |
| Improvement | 14 (34) | |
| Autoimmunity 25 (59) | Complete remission | 11 (44) |
| Persistent | 14 (56) | |
| Treatment 26 (48) | Stopped | 12 (46) |
| Persistent | 14 (54) | |