Table 2

AI manifestations in ALPS-FAS and sFAS patients (N = 90)

Any AI manifestations (n = 77 in 55 patients) 
    1 AI manifestation 37 
    2 AI manifestations 14 
    3 AI manifestations 
AI cytopenias (n = 60 in 47 patients) 
    AIHA 30 
    ITP 23 
    AIN 
    Monocytopenia 36 
    Bicytopenia 
    Tricytopenia 
Other AI manifestations (n = 16 in 12 patients) 
    Glomerulonephritis 
    Autoimmune hepatitis 
    Vasculitis 
    Uveitis 
    Aplastic anemia 
    Chronic pancreatitis 
    Severe osteopenia 
    Angioedema 
    Transient alopecia 
Any AI manifestations (n = 77 in 55 patients) 
    1 AI manifestation 37 
    2 AI manifestations 14 
    3 AI manifestations 
AI cytopenias (n = 60 in 47 patients) 
    AIHA 30 
    ITP 23 
    AIN 
    Monocytopenia 36 
    Bicytopenia 
    Tricytopenia 
Other AI manifestations (n = 16 in 12 patients) 
    Glomerulonephritis 
    Autoimmune hepatitis 
    Vasculitis 
    Uveitis 
    Aplastic anemia 
    Chronic pancreatitis 
    Severe osteopenia 
    Angioedema 
    Transient alopecia 

AI indicates autoimmune; and AIN, autoimmune neutropenia.

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