AI manifestations in ALPS-FAS and sFAS patients (N = 90)
| Any AI manifestations (n = 77 in 55 patients) | |
| 1 AI manifestation | 37 |
| 2 AI manifestations | 14 |
| 3 AI manifestations | 4 |
| AI cytopenias (n = 60 in 47 patients) | |
| AIHA | 30 |
| ITP | 23 |
| AIN | 7 |
| Monocytopenia | 36 |
| Bicytopenia | 9 |
| Tricytopenia | 2 |
| Other AI manifestations (n = 16 in 12 patients) | |
| Glomerulonephritis | 2 |
| Autoimmune hepatitis | 3 |
| Vasculitis | 4 |
| Uveitis | 1 |
| Aplastic anemia | 2 |
| Chronic pancreatitis | 1 |
| Severe osteopenia | 1 |
| Angioedema | 1 |
| Transient alopecia | 1 |
| Any AI manifestations (n = 77 in 55 patients) | |
| 1 AI manifestation | 37 |
| 2 AI manifestations | 14 |
| 3 AI manifestations | 4 |
| AI cytopenias (n = 60 in 47 patients) | |
| AIHA | 30 |
| ITP | 23 |
| AIN | 7 |
| Monocytopenia | 36 |
| Bicytopenia | 9 |
| Tricytopenia | 2 |
| Other AI manifestations (n = 16 in 12 patients) | |
| Glomerulonephritis | 2 |
| Autoimmune hepatitis | 3 |
| Vasculitis | 4 |
| Uveitis | 1 |
| Aplastic anemia | 2 |
| Chronic pancreatitis | 1 |
| Severe osteopenia | 1 |
| Angioedema | 1 |
| Transient alopecia | 1 |
AI indicates autoimmune; and AIN, autoimmune neutropenia.