AI manifestations in ALPS-FAS and sFAS patients (N = 90)
Any AI manifestations (n = 77 in 55 patients) | |
1 AI manifestation | 37 |
2 AI manifestations | 14 |
3 AI manifestations | 4 |
AI cytopenias (n = 60 in 47 patients) | |
AIHA | 30 |
ITP | 23 |
AIN | 7 |
Monocytopenia | 36 |
Bicytopenia | 9 |
Tricytopenia | 2 |
Other AI manifestations (n = 16 in 12 patients) | |
Glomerulonephritis | 2 |
Autoimmune hepatitis | 3 |
Vasculitis | 4 |
Uveitis | 1 |
Aplastic anemia | 2 |
Chronic pancreatitis | 1 |
Severe osteopenia | 1 |
Angioedema | 1 |
Transient alopecia | 1 |
Any AI manifestations (n = 77 in 55 patients) | |
1 AI manifestation | 37 |
2 AI manifestations | 14 |
3 AI manifestations | 4 |
AI cytopenias (n = 60 in 47 patients) | |
AIHA | 30 |
ITP | 23 |
AIN | 7 |
Monocytopenia | 36 |
Bicytopenia | 9 |
Tricytopenia | 2 |
Other AI manifestations (n = 16 in 12 patients) | |
Glomerulonephritis | 2 |
Autoimmune hepatitis | 3 |
Vasculitis | 4 |
Uveitis | 1 |
Aplastic anemia | 2 |
Chronic pancreatitis | 1 |
Severe osteopenia | 1 |
Angioedema | 1 |
Transient alopecia | 1 |
AI indicates autoimmune; and AIN, autoimmune neutropenia.