WHO systemic mastocytosis variants
| Variant term . | Subvariants . |
|---|---|
| Cutaneous mastocytosis (CM) | Urticaria pigmentosa (UP), maculopapular CM (MPCM), diffuse CM (DCM), mastocytoma of skin |
| Indolent systemic mastocytosis (ISM) | Smoldering SM, isolated bone marrow mastocytosis |
| Systemic mastocytosis with an associated clonal hematologic non–mast cell lineage disease (SM-AHNMD) | SM-AML, SM-MDS, SM-MPD, SM-CMML, SM-NHL |
| Aggressive systemic mastocytosis (ASM) | |
| Mast cell leukemia (MCL) | Aleukemic MCL |
| Mast cell sarcoma | |
| Extracutaneous mastocytoma |
| Variant term . | Subvariants . |
|---|---|
| Cutaneous mastocytosis (CM) | Urticaria pigmentosa (UP), maculopapular CM (MPCM), diffuse CM (DCM), mastocytoma of skin |
| Indolent systemic mastocytosis (ISM) | Smoldering SM, isolated bone marrow mastocytosis |
| Systemic mastocytosis with an associated clonal hematologic non–mast cell lineage disease (SM-AHNMD) | SM-AML, SM-MDS, SM-MPD, SM-CMML, SM-NHL |
| Aggressive systemic mastocytosis (ASM) | |
| Mast cell leukemia (MCL) | Aleukemic MCL |
| Mast cell sarcoma | |
| Extracutaneous mastocytoma |