Patient demographics, age, genetic mutation, immune status, and influenza vaccination
Patient . | Age, y . | Mutation . | TLC . | % CD3 . | % CD4 . | % CD8 . | % CD19 . | TCF . | Year of flu vaccination . |
---|---|---|---|---|---|---|---|---|---|
XLA 1 | 23 | R28C | 2.0 | 93 | 56 | 32 | < 1 | NA | 2002 |
XLA 2 | 27 | E636X | 2.2 | 95 | 64 | 28 | < 1 | Normal | 2005 |
XLA 3 | 24 | E636X | 2.2 | 95 | 67 | 26 | < 1 | Normal | 2005 |
XLA 4 | 23 | E636X | 2.1 | 95 | 69 | 22 | < 1 | Normal | 2005 |
XLA 5 | 36 | R28C | 0.8 | 95 | 32 | 53 | < 1 | Normal | 2005 |
XLA 6 | 24 | R28C | 1.5 | 92 | 50 | 26 | < 1 | NA | NA |
XLA 8 | 38 | R28C | 2.0 | 70 | 55 | 19 | 2 | NA | 2005 |
X-HIM 1 | 37 | 560delA | 0.9 | 74 | 48 | 23 | 2 | NA | NA |
X-HIM 2 | 55 | 148T>C, 617T>A, and 618C>T | 1.6 | 75 | 47 | 23 | 11 | Normal | 2006 |
Patient . | Age, y . | Mutation . | TLC . | % CD3 . | % CD4 . | % CD8 . | % CD19 . | TCF . | Year of flu vaccination . |
---|---|---|---|---|---|---|---|---|---|
XLA 1 | 23 | R28C | 2.0 | 93 | 56 | 32 | < 1 | NA | 2002 |
XLA 2 | 27 | E636X | 2.2 | 95 | 64 | 28 | < 1 | Normal | 2005 |
XLA 3 | 24 | E636X | 2.2 | 95 | 67 | 26 | < 1 | Normal | 2005 |
XLA 4 | 23 | E636X | 2.1 | 95 | 69 | 22 | < 1 | Normal | 2005 |
XLA 5 | 36 | R28C | 0.8 | 95 | 32 | 53 | < 1 | Normal | 2005 |
XLA 6 | 24 | R28C | 1.5 | 92 | 50 | 26 | < 1 | NA | NA |
XLA 8 | 38 | R28C | 2.0 | 70 | 55 | 19 | 2 | NA | 2005 |
X-HIM 1 | 37 | 560delA | 0.9 | 74 | 48 | 23 | 2 | NA | NA |
X-HIM 2 | 55 | 148T>C, 617T>A, and 618C>T | 1.6 | 75 | 47 | 23 | 11 | Normal | 2006 |
TCF indicates T-cell function in response to phytohemagglutinin; TLC, total lymphocyte count; and NA, not available.