Clinical and Laboratory Data of Patients With Hereditary Spherocytosis
Patients . | Age . | Hemoglobin . | MCV . | MCHC . | Reticulocytes . | Spectrin/band 3* . | 2.1/band 3† . | Relative Protein Content . |
---|---|---|---|---|---|---|---|---|
. | (yr) . | g/dL . | FL . | g/dL . | ×109/L . | . | . | . |
I.1 | 58 | 13.4 | 87 | 32.9 | 416.5 | 1.28 | 0.25 | 78% Band 3 |
II.1 | 36 | 12.4 | 91 | 32.5 | 544.70 | 1.34 | 0.28 | 75% Band 3 |
II.2 | 32 | 12.7 | 87 | 33.3 | 543.12 | 1.26 | 0.25 | 79% Band 3 |
3‡ | 38 | 14.7 | 85 | 35.0 | 137.80 | 1.42 | 0.30 | 70% Band 3 |
4‡ | 32 | 14.5 | 92 | 32.1 | 98.20 | 1.26 | 0.26 | 79% Band 3 |
5‡ | 20 | 13.7 | 78 | 35.6 | 59.28 | 1.00 | 0.14 | 70% Ankyrin |
Patients . | Age . | Hemoglobin . | MCV . | MCHC . | Reticulocytes . | Spectrin/band 3* . | 2.1/band 3† . | Relative Protein Content . |
---|---|---|---|---|---|---|---|---|
. | (yr) . | g/dL . | FL . | g/dL . | ×109/L . | . | . | . |
I.1 | 58 | 13.4 | 87 | 32.9 | 416.5 | 1.28 | 0.25 | 78% Band 3 |
II.1 | 36 | 12.4 | 91 | 32.5 | 544.70 | 1.34 | 0.28 | 75% Band 3 |
II.2 | 32 | 12.7 | 87 | 33.3 | 543.12 | 1.26 | 0.25 | 79% Band 3 |
3‡ | 38 | 14.7 | 85 | 35.0 | 137.80 | 1.42 | 0.30 | 70% Band 3 |
4‡ | 32 | 14.5 | 92 | 32.1 | 98.20 | 1.26 | 0.26 | 79% Band 3 |
5‡ | 20 | 13.7 | 78 | 35.6 | 59.28 | 1.00 | 0.14 | 70% Ankyrin |