Table 1.

Coagulation and FVII Antigen Indices of the FVII (N57D) Kindred

Subject Exon 4 GenotypeLaboratory 1* Laboratory 2*
FVII:Ag (%) FVII:C (U/mL) FVII:Ag (%)FVII:C (U/mL)
II1 H  96  0.75  97 0.71  
III2 H  102  0.67  92  0.66 
III3†  H  51  0.32  72  0.37 
IV3 H  86  0.57  80  0.60  
Mean‡  84  0.58  85  0.59 
Subject Exon 4 GenotypeLaboratory 1* Laboratory 2*
FVII:Ag (%) FVII:C (U/mL) FVII:Ag (%)FVII:C (U/mL)
II1 H  96  0.75  97 0.71  
III2 H  102  0.67  92  0.66 
III3†  H  51  0.32  72  0.37 
IV3 H  86  0.57  80  0.60  
Mean‡  84  0.58  85  0.59 

Abbreviation: H, heterozygous.

F0-150

Experiments were performed on both identical fresh plasma samples and a single lot of normal pooled plasma by two independent laboratories. All values are compared to normal pooled plasma which was assigned values of 100% FVII:Ag and 1 unit/ml FVII:C activity.

F0-151

Propositus.

F0-152

The mean of FVII antigen and coagulant activities from affected family members.

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