Laboratory Data in TTP Patients
Patient . | Born . | Blood Sample . | Date . | Platelets . | vWF:RCof . | vWF:Ag . | vWF:RCof/Ag . | Hb (g/dL) . |
---|---|---|---|---|---|---|---|---|
. | . | . | (mo/d/yr) . | (×10−9/L) . | (U/mL) . | (U/mL) . | . | . |
A1, propositus, TTP | 1964 | 1 | 1/4/96 | 79 | 2.06 | 1.87 | 1.10 | 12.4 |
2 | 4/24/96 | 110 | 1.94 | 1.81 | 1.07 | 13.5 | ||
A2, brother, TTP | 1975 | 1 | 1/4/96 | 175 | 2.83 | 1.81 | 1.56 | 14.4 |
2 | 5/4/96 | 247 | 1.42 | 1.40 | 1.01 | 14.9 | ||
A3, father, asymptomatic | 1939 | 1 | 1/4/96 | 244 | 1.62 | 1.53 | 1.06 | 14.6 |
2 | 4/5/96 | 244 | 1.50 | 1.36 | 1.10 | 16.2 | ||
A4, mother, asymptomatic | 1941 | 1 | 1/4/96 | 295 | 1.88 | 1.58 | 1.19 | 11.9 |
2 | 4/5/96 | 271 | 1.73 | 1.79 | 0.97 | 13.5 | ||
A5, sister, asymptomatic | 1967 | 1 | 12/27/95 | 265 | 1.26 | 1.27 | 0.99 | 14.5 |
B, propositus, TTP | 1958 | 1 | 2/20/96 | 45 | 1.67 | 1.76 | 0.95 | 14.0 |
2 | 4/24/96 | 278 | 1.22 | 0.95 | 1.28 | 15.0 | ||
C, proposita, TTP | 1963 | 1 | 3/1/93 | 159 | 1.38 | 1.77 | 0.78 | 13.7 |
2 | 4/22/96 | 187 | 1.53 | 1.31 | 1.17 | 13.7 | ||
Normal range | — | — | — | 125-320 | 0.5-1.5 | 0.5-1.5 | 0.64-1.36* | 13.5-16.8 (M) |
12.1-15.4 (F) |
Patient . | Born . | Blood Sample . | Date . | Platelets . | vWF:RCof . | vWF:Ag . | vWF:RCof/Ag . | Hb (g/dL) . |
---|---|---|---|---|---|---|---|---|
. | . | . | (mo/d/yr) . | (×10−9/L) . | (U/mL) . | (U/mL) . | . | . |
A1, propositus, TTP | 1964 | 1 | 1/4/96 | 79 | 2.06 | 1.87 | 1.10 | 12.4 |
2 | 4/24/96 | 110 | 1.94 | 1.81 | 1.07 | 13.5 | ||
A2, brother, TTP | 1975 | 1 | 1/4/96 | 175 | 2.83 | 1.81 | 1.56 | 14.4 |
2 | 5/4/96 | 247 | 1.42 | 1.40 | 1.01 | 14.9 | ||
A3, father, asymptomatic | 1939 | 1 | 1/4/96 | 244 | 1.62 | 1.53 | 1.06 | 14.6 |
2 | 4/5/96 | 244 | 1.50 | 1.36 | 1.10 | 16.2 | ||
A4, mother, asymptomatic | 1941 | 1 | 1/4/96 | 295 | 1.88 | 1.58 | 1.19 | 11.9 |
2 | 4/5/96 | 271 | 1.73 | 1.79 | 0.97 | 13.5 | ||
A5, sister, asymptomatic | 1967 | 1 | 12/27/95 | 265 | 1.26 | 1.27 | 0.99 | 14.5 |
B, propositus, TTP | 1958 | 1 | 2/20/96 | 45 | 1.67 | 1.76 | 0.95 | 14.0 |
2 | 4/24/96 | 278 | 1.22 | 0.95 | 1.28 | 15.0 | ||
C, proposita, TTP | 1963 | 1 | 3/1/93 | 159 | 1.38 | 1.77 | 0.78 | 13.7 |
2 | 4/22/96 | 187 | 1.53 | 1.31 | 1.17 | 13.7 | ||
Normal range | — | — | — | 125-320 | 0.5-1.5 | 0.5-1.5 | 0.64-1.36* | 13.5-16.8 (M) |
12.1-15.4 (F) |
Abbreviations: M, male; F, female.
As determined from measurements in 145 subjects with normal vWF values.