Complement Measurements in 24 Patients With HAE and 6 Patients With AAE
| . | C1-Inhibitor . | C1-Inhibitor . | C4 Antigen % . |
|---|---|---|---|
| . | Function % . | Antigen % . | . |
| HAE Type I (n = 13) | 22 (<10-42) | 19 (<10-39) | 20 (<10-56) |
| HAE Type II (n = 11) | 19 (<10-32) | 185 (54-205) | 16 (<10-51) |
| AAE (n = 6) | <10 | 25 (<10-39) | <10 |
| Normal ranges | (70-130) | (70-130) | (60-140) |
| . | C1-Inhibitor . | C1-Inhibitor . | C4 Antigen % . |
|---|---|---|---|
| . | Function % . | Antigen % . | . |
| HAE Type I (n = 13) | 22 (<10-42) | 19 (<10-39) | 20 (<10-56) |
| HAE Type II (n = 11) | 19 (<10-32) | 185 (54-205) | 16 (<10-51) |
| AAE (n = 6) | <10 | 25 (<10-39) | <10 |
| Normal ranges | (70-130) | (70-130) | (60-140) |
HAE patients are divided into type I (low levels of both antigenic and functional C1-inhibitor) and type II (low levels of functional C1-inhibitor only). Data are reported as median values (ranges in parenthesis). Results are expressed as percent of a normal human pooled plasma.