Patients' Features
| Features . | Patient M.F. . | Patient N.F. . | Patient S.F. . |
|---|---|---|---|
| Age | 5 yr 11 mo | 13 yr 8 mo | 15 yr 4 mo |
| Splenomegaly | +++ | +++ | ++ |
| (age at onset) | 1 mo | 1 yr 6 mo | 1 yr |
| Lymphoadenopathy | +++ | ++ | ++ |
| IgG (g/L) | 41.8 | 12.0 | 13.6 |
| IgA (g/L) | 5.5 | 2.1 | 2.9 |
| IgM (g/L) | 1.4 | 0.8 | 1.2 |
| Autoimmunity: | |||
| Clinical features | None | AHA, thrombocytopenia | None |
| Autoantibodies | ANA, APL | APL, APA | ANA, APL |
| Features . | Patient M.F. . | Patient N.F. . | Patient S.F. . |
|---|---|---|---|
| Age | 5 yr 11 mo | 13 yr 8 mo | 15 yr 4 mo |
| Splenomegaly | +++ | +++ | ++ |
| (age at onset) | 1 mo | 1 yr 6 mo | 1 yr |
| Lymphoadenopathy | +++ | ++ | ++ |
| IgG (g/L) | 41.8 | 12.0 | 13.6 |
| IgA (g/L) | 5.5 | 2.1 | 2.9 |
| IgM (g/L) | 1.4 | 0.8 | 1.2 |
| Autoimmunity: | |||
| Clinical features | None | AHA, thrombocytopenia | None |
| Autoantibodies | ANA, APL | APL, APA | ANA, APL |
Abbreviations: AHA, autoimmune hemolytic anemia; ANA, antinuclear antibody; APL, antiphospholipid antibody; APA, antiplatelet antibody.