Clinical Characteristics of PNH Patients
ID . | Age (yr) . | Sex . | Diagnosis . | Duration (yr)* . | Hemoglobin (mg/μL) . | ANC (per μL) . | Plt (×103/μL) . | Ham's % . | BM Biopsy . |
---|---|---|---|---|---|---|---|---|---|
1 | 56 | M | AA | 9 | 7.9 | 730 | 7 | 2 | Normo |
2 | 63 | F | MDS | 6 | 9.1 | 990 | 26 | 20 | Hypo |
3 | 35 | F | AA | 5 | 5.5 | 250 | 29 | 58 | Hypo |
4 | 37 | M | AA | 18 | 8.7 | 2,500 | 9 | 20 | Hypo |
5 | 49 | M | MDS | 2 | 10.3 | 1,500 | 67 | 33 | Hypo |
6 | 24 | F | AA | 3 | 11 | 3,000 | 57 | 11 | Hypo |
7 | 24 | M | AA | 4 | 7.1 | 2,500 | 48 | 23 | Hypo |
8 | 30 | F | AA | 7 | 10.5 | 1,900 | 120 | 17 | Normo |
9 | 19 | M | AA | 1 | 9.7 | 3,700 | 25 | 3 | Normo |
10 | 24 | F | AA | 7 | 14 | 4,200 | 88 | 2 | Hypo |
11 | 34 | F | AML | 11 | 6.2 | 20 | 7 | 2 | Hypo |
12 | 43 | F | Hemol | 4 | 9 | 3,500 | 125 | 43 | Hyper |
13 | 56 | F | AA | 3 | 12.8 | 690 | 154 | 7.3 | Hypo |
14 | 16 | F | AA | 6 | 12.3 | 3,540 | 141 | 80 | Normo |
15 | 53 | F | AA | 6 | 9.2 | 2,800 | 23 | 3 | Normo |
16 | 30 | M | Hemol | 1 | 7.7 | 1,610 | 30 | 14 | Normo |
17 | 29 | M | Hemol | 10 | 9.3 | 1,710 | 142 | 38 | Normo |
ID . | Age (yr) . | Sex . | Diagnosis . | Duration (yr)* . | Hemoglobin (mg/μL) . | ANC (per μL) . | Plt (×103/μL) . | Ham's % . | BM Biopsy . |
---|---|---|---|---|---|---|---|---|---|
1 | 56 | M | AA | 9 | 7.9 | 730 | 7 | 2 | Normo |
2 | 63 | F | MDS | 6 | 9.1 | 990 | 26 | 20 | Hypo |
3 | 35 | F | AA | 5 | 5.5 | 250 | 29 | 58 | Hypo |
4 | 37 | M | AA | 18 | 8.7 | 2,500 | 9 | 20 | Hypo |
5 | 49 | M | MDS | 2 | 10.3 | 1,500 | 67 | 33 | Hypo |
6 | 24 | F | AA | 3 | 11 | 3,000 | 57 | 11 | Hypo |
7 | 24 | M | AA | 4 | 7.1 | 2,500 | 48 | 23 | Hypo |
8 | 30 | F | AA | 7 | 10.5 | 1,900 | 120 | 17 | Normo |
9 | 19 | M | AA | 1 | 9.7 | 3,700 | 25 | 3 | Normo |
10 | 24 | F | AA | 7 | 14 | 4,200 | 88 | 2 | Hypo |
11 | 34 | F | AML | 11 | 6.2 | 20 | 7 | 2 | Hypo |
12 | 43 | F | Hemol | 4 | 9 | 3,500 | 125 | 43 | Hyper |
13 | 56 | F | AA | 3 | 12.8 | 690 | 154 | 7.3 | Hypo |
14 | 16 | F | AA | 6 | 12.3 | 3,540 | 141 | 80 | Normo |
15 | 53 | F | AA | 6 | 9.2 | 2,800 | 23 | 3 | Normo |
16 | 30 | M | Hemol | 1 | 7.7 | 1,610 | 30 | 14 | Normo |
17 | 29 | M | Hemol | 10 | 9.3 | 1,710 | 142 | 38 | Normo |
All the patients received transfusion in the course of the disease; no transfusions were administered in the period before immediate PB examination.
Abbreviations: ANC, absolute neutrophil count; Plt, platelets; AML, acute myelogenous leukemia; Hemol, hemolysis; Normo, normocellular BM; Hypo, hypocellular BM; Hyper, hypercellular BM.
Time from the initial diagnosis.